ORBITAL VENOUS LYMPHATIC MALFORMATION : REVIEWING THE CLINICORADIOLOGICAL ASPECT OF A LESS KNOWN ENTITY.

Abstract

Hemangiomas and venous lymphatic malformations are the two most common orbital vascular lesions seen in pediatric patients. Orbital venouslymphatic malformations (OVLMs) (previously referred to as ′lymphangiomas′) are relatively less common, benign cystic type I vascular malformations. OVLMs may remain clinically unapparent or might manifest in late childhood with slowly progressive proptosis, periorbital swelling and displacement of globe. These malformations usually enlarge gradually. Sudden proptosis may be seen with spontaneous intraorbital hemorrhage or venous thrombosis. Acute presentation includes severe pain, compressive optic neuropathy or loss of vision, when intervention is indicated. Imaging plays critical role in diagnosis. The imaging mainstay is based on USG with high resolution probes and MRI with contrast.