Nevus lipomatosus cutaneus superficialis associated with nevus sebaceous of Jadassohn

Abstract

Sir,Nevus lipomatosus cutaneous superficialis is an uncommon disease of unknown etiology characterized by lipocyte collections situated ectopically within the dermis. Hoffman and Zurhelle first described nevus lipomatosus cutaneous superficialis, (which is also termed pedunculated lipofibroma), in 1921. The typical presentation is as clustered, multiple skin-coloured or yellowish papules or nodules present on the lower trunk, especially on the buttocks. Two types of nevus lipomatosus cutaneous superficialis are defined: the multiple or classic type consists of zonal or segmentally distributed multiple lesions while the solitary type presents as a solitary papule or nodule. [1]A 21-year-old man presented to our clinic with many asymptomatic nodular lesions distributed in a segmental pattern on the left buttock and left lumbar area. The lesion began 10 years ago and was gradually increasing in size. On dermatologic examination, multiple, skin-colored, soft coalescent papules and nodular lesions were observed in an approximately 15 × 25 cm area in the left sacral and left lumbar region. The lesions were unilateral and did not cross the midline. A 5 × 11 cm diameter flesh-colored, soft to firm, lobulated and smooth surfaced, non-tender, rubbery, sessile cerebriform