Hairy nevus lipomatosus cutaneous superficialis: A rare presentation

Abstract

Abstract Nevus lipomatosis cutaneous superficialis (NLCS) is a rare hamartoma of mature adipose tissue. There are two main clinical variants: one with multiple lesions that are usually presented in a segmental distribution, and another variant with a solitary papule or nodule. However, rare cases have also been published to describe other clinical presentations, such as giant NLCS, NLCS with multiple open comedones, and NLCS with ulcerations and necrosis. One report has described increased hair growth over the nevus. The present report describes a case of a child with NLCS with an unusual presentation of overlying hypertrichosis.