Abstract
Supravalvular mitral stenosis is a rare condition characterized by an abnormal ridge, with one or two orifices, covering and obstructing the mitral valve. Preoperative diagnosis is difficult with transtoracic echo (TTE), angiography and magnetic resonance imaging (MRI).In this case, a 36-year-old male, was admitted to our Heart department: He experienced progressive dyspnea on effort and at rest.Diagnosis was made by transesophageal echocardiography which showed, on apical 4-chamber section, an anulare structure attached since a membrane to the atrial wall anterior mitral valve leaflet and just proximal to the posterior mitral leaflet.Pre-operative identification of the supravalvular mitral ring is the target for obtaining good surgical results. Cineangiography and MRI both failed in reaching this objective, whereas, transesophageal echocardiography is the best method to identify this congenital heart disease.Using TEE the identification is not only possible but also easier.
Highlights
Mitral supravalvular ring is a rare congenital heart defect, as descibed by Fisher [1], characterized by an abnormal ridge of connective tissue on the atrial side of the mitral valve
Pre-operative identification of the supravalvular mitral ring is the target for obtaining good surgical results
Cineangiography and magnetic resonance imaging (MRI) both failed in reaching this objective, whereas, transesophageal echocardiography is the best method to identify this congenital heart disease
Summary
Mitral supravalvular ring is a rare congenital heart defect, as descibed by Fisher [1], characterized by an abnormal ridge of connective tissue on the atrial side of the mitral valve. TtmlFeuEiairgtEferlueasartlhtevtoa2wclvheeedld,eoalifnkleeatpaaicnmadlejm4u-sbcthrapanrmoebxteiomr tsahelectotaiottrnhia,elapwnoaaslntleuarlnaiotrersrtimoruritcr-al TEE showed, on apical 4-chamber section, an anular structure attached like a membrane to the atrial wall anterior mitral valve leaflet and just proximal to the posterior mitral leaflet. Based on this diagnosis, the patient underwent a transesophageal-echo (TEE). The echocardiogram (TTE) showed left ventricular enlargment, atrial dilatation, moderate/severe mitral regurgitation and moderate aortic regurgitation; mitral valve masses were suspected. This supravalvular ring was proximal to the left atrial appendage, in contradistinction to "cor triatriatum"; it restricted the leaflets movement and impaired their opening.
Sign-in/Register to view highlights & summary Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
