Large non restrictive apical ventricular septal defect curtailed by anomalous right ventricular muscle band : An rare variant double chambered right ventricle

Abstract

Anomalous muscle bands in right ventricle are uncommon findings with variable clinical presentations. We report an interesting case of a 6 year old asymptomatic boy with a large apical non restrictive ventricular septal defect and an anomalous muscle band in right ventricle. The muscle band divided the right ventricle into 2 chambers: smaller apical chamber which was connected to the left ventricle by an large apical non restrictive ventricular septal defect and proximal chamber which included right ventricular inflow and outflow tract. The hemodynamic burden of the ventricular septal defect was curtailed by the restrictive muscle band, hence patient remained asymptomatic. In total the condition behaved like a restrictive ventricular septal defect. Patient was kept under follow up and was not considered for surgical correction in view of negligible hemodynamic disturbances. Previously in literature 1 such case has been reported earlier Key words: Double chambered right ventricle, Right ventricular anomalous muscle band, Ventricular septal defect