Isolated right ventricular endomyocardial fibrosis in a young male with chronic myeloid leukemia (RCD code: III-3F.2)

Abstract

Endomyocardial fibrosis (EMF) is a rare disease of unknown etiology which is more prevalent in tropical countries. EMF is associated with fibrosis of endomyocardium, involving one or both ventricles. It usually presents with heart failure and has a poor prognosis. The diagnosis is usually made on echocardiogram, however cardiac magnetic resonance (CMR) is ideal for the diagnosis of EMF. We report a rare case of right ventricular endomyocardial fibrosis in a young male with chronic myeloid leukemia but no eosinophilia. Right ventricular EMF was diagnosed on the basis of classic findings on CMR. JRCD 2017; 3 (3): 98–100.