Herlyn-Werner-Wunderlichov sindrom s piohematokolposom

Abstract

Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare malformation syndrome of the women reproductive tract characterized by uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. We report here a case of a 20 year-old patient presented to the emergency department with pain in the right lower quadrant. The clinical exam showed a vaginal fluctuant painful mass obliterating the right part of the vagina. Transvaginal ultrasound showed uterus didelphys, the right uterus was dilated with a dense fluid collection which corresponded to pyohematometra. It also revealed a dense vaginal collection which corresponded to pyohematocolpos. Abdominal ultrasound showed the absence of a right kidney. The laparoscopy showed uterus didelphys with a large right uterus. We performed the resection of the vaginal septum to reconstruct one vagina. The first follow-up visit revealed a healthy wound with no adhesion of the vaginal wall. Prompt and accurate diagnosis of female reproductive tract disorders, including HWWS, is necessary to prevent complications and preserve future fertility.