Fibrous Dysplasia of the Temporal Bone: A Case Series

Abstract

Fibrous dysplasia (FD) is a benign and chronic abnormal proliferation of fibrous tissue and bone. It presents as a growth; however, most authors do not consider it to be true neoplasia. Despite its affinity to affect craniofacial bones, it usually remains asymptomatic and, sometimes, presents with deformity. Owing to its rarity, diagnostic difficulty, scarce literature, and staggered opinions on optimal management, it still interests otolaryngologists. FD involving temporal bone is even rarer. The most common initial findings are stenosis of the external auditory canal and conductive hearing loss. Most cases involve a single bone; however, about 20% of patients have polyostotic involvement often with extraosseous abnormalities. This disease produces widely variable radiographic images. Radio imaging is highly suggestive; however, the diagnosis is clinched only by histopathology with a surgical specimen. Here, we present a series of two cases of temporal bone FD with its management and outcomes.