Abstract
Fibrous dysplasia is a benign lesion, congenital, recurrent character and etiology unknown, caused by a bone modeling disorder with constant alterations of the normal bone being replaced by immature fibrous tissue. The lesion may involve one or more bones being the maxilla the facial bone more affected. We report a case of polyostotic fibrous dysplasia in a male patient complaining of increased volume in the right genital region. In this case, Computed Tomography (CT) was the main radiographic examination to demonstrate the extension and radiodensity that the lesion assumes in the craniofacial bones, being therefore of fundamental importance in the surgical planning and in the longitudinal follow-up of the operated patient. The diagnosis was confirmed by anatopathology and the treatment of choice was osteoplasty. This article also aims to review the main clinical, radiological, histopathological, differential diagnosis and Fibrous dysplasia treatment.
Highlights
Fibrous Dysplasia (FD) is described as a slowly evolving, benign tumour disorder of bone development characterized by the replacement of normal bone by excessive proliferation of cellular fibrous connective tissue interspersed with irregular bone trabeculae [1,2].In 1891, Von Recklinghausen denominated de “generalist fibrous osteitis” pathological conditions that characterized deformities and bone alterations [3,4]
Fibrous dysplasia is a benign lesion, congenital, recurrent character and etiology unknown, caused by a bone modeling disorder with constant alterations of the normal bone being replaced by immature fibrous tissue
We report a case of polyostotic fibrous dysplasia in a male patient complaining of increased volume in the right genital region
Summary
Fibrous Dysplasia (FD) is described as a slowly evolving, benign tumour disorder of bone development characterized by the replacement of normal bone by excessive proliferation of cellular fibrous connective tissue interspersed with irregular bone trabeculae [1,2].In 1891, Von Recklinghausen denominated de “generalist fibrous osteitis” pathological conditions that characterized deformities and bone alterations [3,4]. Only in 1938, Liechtenstein and Jaffe recognized these conditions described, previously, as a well-characterized disease and named it fibrous dysplasia [5,6]. The etiology of this entity is still unknown [7,8]. The monostotic form shows no predilection for sex and is found in about 70% of all cases of fibrous dysplasia, with gnathic bones being the most commonly affected sites [10]. The cases of monostotic fibrous dysplasia are usually diagnosed during the second decade of life, with painless swelling being the most common feature [1,2]
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