A rare case report of fibrous dysplasia of maxillary bone causing progressive vision loss: Case report

Abstract

Fibrous dysplasia is a benign tumor of bone, uncommonly affecting the maxilla, congenital, recurrent character and etiology unknown, caused by a bone modeling disorder in which normal bone is replaced by immature fibrous tissue. The lesion may involve one or more bones being the maxilla the facial bone more affected. We report a case of monostotic variety fibrous dysplasia in a male patient complaining of progressive swelling in rt maxilla that compress the inferior orbital bone and finally produce significant loss of vision. In this case, Computed Tomography (CT) was the main radiographic examination to demonstrate the extension and radiodensity that the lesion assumes in the craniofacial bones, being therefore of fundamental importance in the surgical planning and in the longitudinal follow-up of the operated patient. The diagnosis was confirmed by anatopathology and the treatment of choice was removal of the tumor [total maxillectomy in this case followed by reconstruction of palate and defect. This article also aims to review the main clinical, radiological, histopathological, differential diagnosis and Fibrous dysplasia treatment.