Ewing’s Sarcoma of the Adrenal Gland; A Rare Extraosseous Presentation

Abstract

Ewing sarcoma also known as peripheral primitive neuroectodermal tumors (ES/PPNETs) usually produce in the chest wall, extraosseous soft tissues, and long or flat bones, however only rarely in solid organs. Although they can develop in any part of the body, development in the adrenal glands is very uncommon. We present a case of Ewing sarcoma (PNET) of the adrenal gland and the extraordinary diagnostic and therapeutic challenges faced during its diagnosis. Early detection of extraosseous disease with radiological imaging and the multimodality treatment strategy lowers morbidity and death in Ewing’s sarcoma of the adrenal gland.