Abstract
Palmoplantar keratodermas (PPKs) represent a diverse group of hereditary and acquired disorders characterized by hyperkeratosis of the skin on the palms and soles [1]. The three major patterns of involvement are diffuse, focal and punctate. There are clinical distinguishing features for each disease in this group, for example, transmigration to areas beyond the palmoplantar skin. Also the extent of associated systemic symptoms if present help in characterization of each type. Although a number of classifications of keratodermashave been published, none unite satisfactorily clinical presentation, pathology and molecular pathogenesis. We based our concise review of selected eponyms linked to PPK (Tabl. I) [2-36], on the classifications published in the current editions of two major textbooks in dermatology; Rook’s Textbook of Dermatology and Dermatology by Jean L Bolognia. EPONYMS IN THE DERMATOLOGY LITERATURE LINKED TO PALMO-PLANTAR KERATODERMA
Highlights
Palmoplantar keratodermas (PPKs) represent a diverse group of hereditary and acquired disorders characterized by hyperkeratosis of the skin on the palms and soles [1]
This syndrome is characterized by knuckle pads,leukonychia, palmoplanter keratoderma (PPK) andsensorineural deafness
In 1965, Dr Salim Haim (1919-1983), (Fig. 11), dermatologist and Dr Munk, a radiologist, from Haifa reported this rsyndrome, which is characterized by palmoplantar keratosis, pes planus, onychogryphosis periodontitis, arachnodactyly, and acroosteolysis
Summary
Palmoplantar keratodermas (PPKs) represent a diverse group of hereditary and acquired disorders characterized by hyperkeratosis of the skin on the palms and soles [1]. This syndrome is characterized by knuckle pads,leukonychia, palmoplanter keratoderma (PPK) andsensorineural deafness. It is a type of focal Palmoplantar Keratoderma (Isolated). CarvajalHuerta (1998) described 18 patients with a confirmation of epidermolytic palmoplantar keratoderma, woolly hair, and dilated cardiomyopathy, examined clinically and histologically in Ecuador between 1970 and 1997. ND is a rare autosomal recessive inherited association of right ventricular dysplasia/dilated cardiomyopathy with woolly hair and palmoplantar keratoderma.
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