EP10.25: A specific prenatal 2D sonographic feature of truncus arteriosus and pulmonary atresia with ventricular septal defect: the Chinese vase sign

Abstract

We wanted to share two cases which heart anomaly was found by a single great artery in left ventricular outflow tract (LVOT) at the beginning. One was terminated at 21 weeks 6 days gestational age with final diagnosis of persistent truncus arteriosus (PTA). The other was delivered by Caesarean section at 38 weeks gestational age with final diagnosis of pulmonary atresia with ventricular septal defect (PA-VSD) and tricuspid atresia. The heart anomaly of both cases was revealed by a single great artery in LVOT. According to heart embryology, PTA is thought to result from incomplete or failed septation of the embryonic truncus arteriosus. PA is happened when pulmonary valve did not form at all, and no blood can go from the right ventricle of the heart out to the lungs. Both PTA and PA-VSD are characterised by a single great vessel emanating from the heart. The embryonic truncus arteriosus and the relatively larger diameter of aorta in PA-VSD present a single great artery in LVOT. We proposed the term “Chinese vase sign” for indentifying a single great artery in LVOT, which suggested the abnormality of artery trunks despite deceivingly normal four chamber views. Further differential diagnostic procedure between persistent truncus arteriosus and pulmonary atresia with ventricular septal defect was needed after detecting a single great artery in left ventricular outflow tract because both PTA and PA-VSD may result in cyanotic baby which need surgical intervention after birth. Supporting information can be found in the online version of this abstract Please note: The publisher is not responsible for the content or functionality of any supporting information supplied by the authors. Any queries (other than missing content) should be directed to the corresponding author for the article.