Abstract
Cerebriform intradermal nevus is a rare form of cutis verticis gyrata. Clinically it manifests as a scalp deformity resembling the surface of the brain, with cerebriform morphologic characteristics these lesions may become malignant or infected. Here we report a 20 year old boy, with cerebriform and soft fold on right temporo-parietal area present since birth. The clinical and histopathological (solitary or clusters of nevus cells) presentations of cerebriform intradermal nevus are described and the therapeutic possibilities discussed. INTRODUCTION: Cutis verticis gyrata (CVG) is a skin deformity characterized by excessive growth of the skin of the scalp, resulting in furrows and folds which are similar to gyri of the brain cortex. CVG can be classified into two forms: 'primary' (essential and non-essential) and 'secondary'. The primary non-essential type is associated with the neurological and ophthalmological changes, while the primary essential form does not present any other disorder except for the cutaneous alterations. Secondary forms of CVG are much more frequent and accompany other pathologies. The treatment consists of local hygiene and surgical resection of skin excess. Intradermal cerebriform nevus is a rare entity, predominantly affecting females at birth or during the first years of life. The condition usually begins with a macular lesion that develops into parietal and occipital symmetric convolutions, occupying one half to three quarters of the scalp6, 7. It has a growth peak at puberty. The mechanism for the cerebriform pattern on the surface of the intradermal cerebriform nevus is unknown. 12
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