Diffuse Cerebral Atrophy, Central Sinus Venous Thrombosis, Hypoplastic Carpus Callosum, Adhd and Vsd in A Child; Anaesthestic Implications

,Narendra Kumar

doi:10.19070/2332-2780-140009

Abstract

Attention deficit hyperkinetic disorder (ADHD ) is characterized by inattention, poor impulse control, motor overactivity and restlessness.The clinical features most commonly seen in patients with hypoplastic carpus callosum syndrome are microcephaly, seizures, developmental delay or retardation, hypotonia, spasticity and multiple somatic anomalies including arthrogryposis, eye anomalies, syringomyelia in the spinal cord and facial dysmorphisms. The response to general anaesthesia with sevoflurane in this rare complex combination of disorders and its postoperative outcomes were observed.

Highlights

Central venous sinus thrombosis (CSVT) in neonates, infants, and children is often multifactorial in etiology, with a predisposing comorbid condition or infirmity identified in up to 95% of those affected1
We report a case of a 2.5 year old female child with diffuse cerebral atrophy, hypoplstic carpus callosum with central sinus venous thrombosis, Attention deficit hyperkinetic disorder (ADHD) and ventricular septal defect posted for sqint surgery of both eyes under general anaesthesia
A 2.5 year old female child weighing 10 kg posted for squint surgery of both eyes under general anaesthesia

Summary

Introduction

Central venous sinus thrombosis (CSVT) in neonates, infants, and children is often multifactorial in etiology, with a predisposing comorbid condition or infirmity identified in up to 95% of those affected1 These conditions include common childhood illnesses such as fever, infection, dehydration, and anemia, as well as acute and chronic medical conditions such as congenital heart disease, nephrotic syndrome, systemic lupus erythematosus and malignancy [1]. We report a case of a 2.5 year old female child with diffuse cerebral atrophy, hypoplstic carpus callosum with central sinus venous thrombosis, ADHD and ventricular septal defect posted for sqint surgery of both eyes under general anaesthesia. At the age of 8 months, she was diagnosed with congenital heart disease having ventricular septal defect with severe pulmonary arterial hypertension, large post tricuspid shunt and cardiac failure. Tracheostomy scar was closed, gradually condition improved and she was discharged after 98 days

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Conclusion