Abstract
Objective To analyze the diagnosis and treatment of embryonal rhabdomyosarcoma of biliary tract in children.Methods The clinical symptoms and treatment of 4 children with embryonal rhabdomyosarcoma of biliary tree were retrospectively reviewed.Results Three boys and one girl,aged from 22 months to 65 months, were diagnosed with embryonic rhabdomyosarcoma of biliary tract.Jaundice presented in all patients.Of the 4 patients, 1 had fever, 1 had abdominal pain, 3 had white feces, and 1 had pruritis; 1 had the right upper abdomen mass, 1 complicated with stones.Two cases were misdiagnosed as hepatitis initially.Tumor recurred and metastasized in one case 1.5 years after operation.One case has stayed alive for 2 months so far.The other 2 cases were lost to follow up.Conclusions Embryonal rhabdomyosarcoma of the biliary tract in children is a rare and poorly prognostic tumor.Ultrasound, abdominal CT scan and MRI are helpful to make the diagnosis.Comprehensive treatments should be carried out to improve the prognosis of this disease. Key words: Rhabdomyosarcoma, embryonal; Biliary tract; Retrospective studies
Published Version
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