Dermatofibrosarcoma protuberans of left temporal area with mass effect causing stenosis of EAM in 66-year-old patient - case report.

Abstract

ABSTRACT INTRODUCTION: Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive cutaneous sarcoma with a low metastasis potential, but a high local recurrence rate. It was first described in 1890 [1]. DFSP grows slowly and may take various forms in clinical trials - it presents both as a firm plaque, subcutaneous fat atrophy and a single or polycyclic tumor. Immunohistochemically DFSP, stains positive for CD34. The gold standard for DFSP treatment is a complete surgical excision with a margin of healthy tissue. Adjuvant therapy includes both radiotherapy and imatinib therapy. CASE REPORT: In June 2022, a 66-year-old patient with a tumor of left temporal area located behind the earlobe was admitted to the medical ward. The skin above the lesion remained unchanged. The imaging examination performed before the procedure showed a well-defined lesion and the results of the FNA biopsy np. BC-73765 were as follows: numerous neoplastic cells, partially fusiform with atypical features, cytological picture does not allow to determine the malignancy of the tumor. After performing the necessary examination, the patient underwent surgery. Histopathological biopsy report of the specimen came out as DFSP. Therefore, the patient was referred for adjuvant radiotherapy by the decision of the Medical Council.CONCLUSIONS: Due to high risk of recurrence and incidence of unclear margins after surgical excision, adjuvant radiotherapy is often used in the treatment of DFSP as it reduces the recurrence rate. KEY WORDS: DFSP, radiotherapy, Mohs micrographic surgery, surgical treatment.