Abstract
Papillon-Lefèvre syndrome (PLS) is a rare disorder characterized by palmar plantar hyperkeratosis and rapidly progressive periodontitis with loss of deciduous and permanent dentition at an early age. It is reported to occur in 1 to 4 individuals per million people. This case report presents highlighting features of the rare PLS in a 17-year old male who complained of discomfort while mastication and it was accompanied with symmetrical, sharply demarcated erythematous plaques involving the skin of the palms and soles, which extended to the finger joints, elbows, and knees. Along with the rough and dry skin, hyperhidrosis of lesion with a foul odor and transverse grooving of nails were noted. The past dental history revealed normal eruption of deciduous teeth followed by pre-mature mobility and shedding in 4-6 months. Permanent teeth also showed normal eruption and early shedding in the next 4-5 years. Complete edentulous maxillary and mandibular arches led to a decrease in alveolar bone and facial heights. There was no similar disorder in the patient’s family but family history revealed the consanguineous marriage of the patient’s parents.
Highlights
Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder character-Correspondence: Sachin C
This report aims at discussing the features of PLS and its management strategies to give an insight to the clinicians and enhance their understanding of this rare disease
The resulting periodontitis is unresponsive to traditional l periodontal treatment and primary ia dentition is exfoliated prematurely by the c age of 4 to 5 years
Summary
Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disorder character-. Metkari,[2] Shilpa Shetty,[3] Savita Thakkannavar,[2] Sachin C. Sarode,[4] Namrata Sengupta,[4] Shankargouda Patil[5]
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