Cloacal Malformation, M??llerian Dysgenesis, Pelvic Organ Prolapse, and Urethrovaginal Fistula in a 17-Year-Old Girl

Abstract

In Brief Background: In contrast to pelvic organ prolapse and urinary incontinence, both cloacal malformations and müllerian dysgenesis are relatively uncommon conditions encountered in the female population. Case: We describe the presentation and surgical management of a 17-year-old girl with combined, complex defects of the genitourinary anatomy, including a common urogenital sinus with imperforate anus, pelvic organ prolapse, uterine didelphys, and urinary incontinence. Conclusion: We discuss the presentation and management of native pelvic organ prolapse in a teenaged patient with müllerian dysgenesis combined with complex cloacal malformations. We believe extensive preoperative preparation and counseling, along with the joint expertise of pediatric urology and urogynecology, resulted in a favorable postoperative outcome for this very challenging patient. A successful surgical reconstruction in a young woman with complex genitourinary anatomy is described.