Centralization of Radial Club Hand

Abstract

Radial club hand, often referred to as radial longitudinal deficiency (RLD), is a rare congenital condition characterized by an underdevelopment and malformation of the radial side structures of the forearm and hand. The anomaly, first described by Petit in 1733, is characterized by a significant shortening of the forearm, radial angulation of the wrist, impaired range of digital motion and limited strength in pinch and grip. In addition, the thumb is always affected with a varying degree of hypoplasia or aplasia. It, encompasses a collection of congenital deformities characterized by hypoplasia of bones, joints, muscles, tendons, ligaments, nerves, and vasculature on the radial aspect of the forearm [1,2]. Radial club hand is a rare condition, occurring in approximately 1 in every 30,000 live births, with a slightly increased incidence in males. The anomaly occurs bilaterally 50% of the time, and is frequently asymmetrical [3].