CASE OF UNILATERAL CONGENITAL AURAL ATRESIA &amp; MICROTIA WITH CHOLESTEATOMA

Cuneyt Kucur,Rahul Kumar Singh,Amber Kesarwani,Amit Goyal,Gaurav Kataria,Dramit Kumar

doi:10.14302/issn.2379-8572.joa-16-1368

Abstract

CASE OF UNILATERAL CONGENITAL AURAL ATRESIA & MICROTIA WITH CHOLESTEATOMA

Highlights

Congenital aural atresia (CAA) refers to a spectrum of ear deformities present at birth that involves some degree of failure of the development of the external auditory canal (EAC)
Cole and Jahrsdorfer (1990) [14] reported the largest series of cholesteatoma and aural stenosis association. They found 48% of their EAC stenosis patients developing cholesteatoma and none of them were under the age of three
All patients presenting with aural atresia and stenosis should be evaluated thoroughly due to their propensity to develop cholesteatoma

Summary

Introduction

Congenital aural atresia (CAA) refers to a spectrum of ear deformities present at birth that involves some degree of failure of the development of the external auditory canal (EAC). The incidence of congenital aural atresia is 1 in 10,000 to 1 in 20,000 live births [1]. Case report : A 13 year old girl presented in ENT outpatient department with complains of recurrent right ear purulent discharge from pre and post auricular area for last 5 years. She had a history of incision and drainage in right post auricular area six months prior for similar complain.

Findings

Discussion

Conclusion