Atlantoaxial subluxation correction using the magerl and brooks techniques in patients with metatropic dysplasia: A report on a case involving siblings

Abstract

BackgroundMetatropic dysplasia (MD) is a form of skeletal dysplasia characterized by short limbs, stature, and kyphoscoliosis. Cervical instability and odontoid hypoplasia are reported as relatively common symptoms; however, surgical treatment is rarely reported. Although upper cervical spine surgery in pediatric patients is challenging because of their peculiar tissue biology, few studies have demonstrated the use of Magerl screws. Case presentationWe describe two sibling cases that were successfully treated for atlantoaxial subluxation of MD using Magerl and Brooks techniques in which bone union of the vertebrae was achieved. C1–C2 fusion surgery for treating atlantoaxial subluxation in pediatric patients with MD is rare. ConclusionsThe present report is doubly remarkable by the unprecedented use of the Magerl and Brooks techniques and because the patients were siblings. The use of the Magerl and Brooks techniques achieved good efficacy, but careful consideration is required in the insertion of transarticular screws.