Aortopulmonary Window, Ventricular Septal Defect, and Membranous Pulmonary Atresia with a Diagnosis of Truncus Arteriosus

Abstract

An infant with aortopulmonary window, ventricular septal defect, membranous pulmonary atresia, right aortic arch, and anomalous origin of the left coronary artery from the pulmonary artery was believed to have persistent truncus arteriosus following cardiac catheterization. Thirty-five percent of patients with aortopulmonary window have coexistent cardiac anomalies; these include ventricular septal defect (7.7 percent), right aortic arch (6.8 percent), anomalous origin of left coronary artery from pulmonary artery (5.1 percent), and patent ductus arteriosus (11 percent). The differential diagnosis of aortopulmonary window and persistent truncus arteriosus is difficult when associated anomalies are present in patients with aortopulmonary window. Evaluation before operation on such patients should include an attempt to delineate coronary arterial origins.