Abstract
BackgroundAnomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare and potential fatal kind of congenital heart disease. This study summarizes the techniques and outcomes of 6 infants with AORPA who underwent the surgical repair.MethodsBetween November 2012 and November 2014, 6 infants with AORPA received surgical repair in the Second Xiangya Hospital and were included in the present study.ResultsSix infants (4 male, 66.7 %) with a median age of 101.5 ± 70.0 days, and a median body weight of 4.13 ± 0.62 kg underwent the surgical repair at our institute. There were no operative, in-hospital or follow-up deaths. Clinical symptoms of all 6 patients relieved at time of discharge, and mean pulmonary artery pressure (MPAP) decreased significantly after surgery. During follow-up, there were no further operations or interventions, mild stenosis at the anastomotic site presented in one patient, and all patients were asymptomatic and in stable clinical condition.ConclusionsThe short and mid-term surgical outcomes of AORPA are excellent in this group of operations. Moreover, we believe the direct implantation to be the optimal surgical strategy for the patients with the proximal form of AORPA.
Highlights
Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare and potential fatal kind of congenital heart disease
AORPA is classified into two subgroups according to the morphological features: proximal and distal forms [2, 3]
About 85 % AORPA are regarded as the proximal form in the report of Kutsche and Van Mierop [3]
Summary
Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare and potential fatal kind of congenital heart disease. This study summarizes the techniques and outcomes of 6 infants with AORPA who underwent the surgical repair. Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare and potentially fatal kind of congenital cardiovascular anomaly, and frequently accompanied with other abnormalities, such as patent ductus arteriosus (PDA), Tetralogy of Fallot (TOF), atrial septal defect (ASD), ventricular septal defect (VSD), and aortic arch isthmus hypoplasia [1]. AORPA is classified into two subgroups according to the morphological features: proximal and distal forms [2, 3]. About 85 % AORPA are regarded as the proximal form in the report of Kutsche and Van Mierop [3]. Xie et al Journal of Cardiothoracic Surgery (2015) 10:97 underwent a successful one-stage surgical correction at our institution in last 2 years
Sign-in/Register to view highlights & summary 
Published Version (
Free)
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call