An Unusual Presentation of a Rare Tumor: Primary Renal Synovial Sarcoma

Abstract

Primary renal synovial sarcomas are very rare and highly aggressive tumors. They are seen at an average age of 35 years. Common symptoms include side pain, abdominal pain, and hematuria. Imaging modalities have no specific findings indicating their presence, and the diagnosis is made based on immunohistochemical methods, which may need to be confirmed by cytogenetic analysis. Radical nephrectomy is the best treatment option currently available, with a combination of anthracyclines and ifosfamidine being administered as adjuvant chemotherapy. In this case report, we present a patient with a primary renal synovial sarcoma presenting with spontaneous massive retroperitoneal bleeding due to tumor rupture. To the best of our knowledge, this is only the second case of such clinical presentation reported in the literature.