Abstract
BackgroundNeuromuscular and vascular hamartoma is a rare lesion of the small intestine, with only 26 cases reported since its initial description in 1982. No occurrence of hamartoma in the appendix has been reported until now.Case presentationA 60-year-old man had been suffering from longstanding right lower quadrant pain. Abdominal computed tomography showed a slight swelling of the appendix as the possible cause of his pain. Laparoscopic appendectomy with partial resection of the cecum was performed for diagnostic and therapeutic purposes. An 18 × 10-mm lesion located on the tip of the appendix was found in the resected specimen. Pathological examination showed that the lesion was covered with normal mucosa and consisted of adipose tissue, smooth muscle fibers, small vessels, and neural fibers. These findings were consistent with neuromuscular and vascular hamartoma of the appendix.ConclusionThis is the first report of neuromuscular and vascular hamartoma arising from the appendix.
Highlights
BackgroundNeuromuscular and vascular hamartoma (NMVH) is a rare lesion of the small intestine, often clinically presenting as non-specific abdominal pain, recurrence of obstructive symptoms, and gastrointestinal bleeding
Neuromuscular and vascular hamartoma is a rare lesion of the small intestine, with only 26 cases reported since its initial description in 1982
This is the first report of neuromuscular and vascular hamartoma arising from the appendix
Summary
Neuromuscular and vascular hamartoma (NMVH) is a rare lesion of the small intestine, often clinically presenting as non-specific abdominal pain, recurrence of obstructive symptoms, and gastrointestinal bleeding. 26 cases have been reported since its initial description, and NMVH occurred in the small intestine in all cases except one, in which it was found in the cecum [1–20]. We report the first case of NMVH of the appendix. Abdominal examination revealed spontaneous pain in the lower right abdomen without rebound tenderness or palpation of a tumor. Abdominal computed tomography (CT) identified a slight swelling of the appendix (about 10 mm) without obvious neoplastic tumors or lymphadenopathy (Fig. 1). Intraoperative findings were a slight swelling of the appendix but no tumor exposure on the serosal surface of the appendix and cecum (Fig. 3). The surgical specimen contained a submucosal lesion located on the tip of the appendix that
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