A Unique Case of Malignant Fibrous Histiocytoma of the Small Intestine with Metastasis of the Bilateral Adrenal Glands and Small Intestine Intussusception

Abstract

We report a unique case of malignant fibrous fibrous histiocytoma of the small intestine with metastasis of the bilateral adrenal glands and intussusception of the small intestine caused by the primary tumor. Malignant fibrous histiocytoma is a common soft tissue neoplasm, but only one case of primary and one case of metastatic malignant fibrous histiocytoma of the gastrointestinal tract producing intussu-sception has ever been reported from the articles available. Our patient was a 60-year-old female who was admitted with the complaints of gastrointestinal upset and body weight loss. Abdominal CT showed bilateral adrenal masses and follow-through small bowel series revealed a filling defect in the jejunum. Repeated CT on CT-guided biopsy revealed mesenteric fat within the lumen of jejunum, which was characteristic of intussusception. Surgery was performed and pathological analysis confirmed primary malignant fibrous histiocytoma with metastasis of the bilateral adrenal glands and intussusception induced by the primary tumor as leading point. We reviewed past articles reporting intussusception in adults and other similar cases available to increase our understanding.