Abstract
30 yrs old man is known to have thalassemia intermedia presented with bilateral lower limb weakness and sphincteric troubles with loss of deep sensations, the motor power of the muscles and precipitancy of urine improved after blood transfusion, laboratory investigations and MRI dorsolumbar spine confirm the diagnosis of extramedullary haematopoiesis.
Highlights
Extramedullary hematopoiesis (EMH) is a rare condition encountered in chronic hemolytic disorders
EMH as a compensatory phenomenon usually develops in the sites involved in hematopoesis during fetal life, such as liver, spleen, and lymph nodes
A paraspinal location for the hematopoietic tissue occurs in 11–15% of patients with EMH
Summary
Extramedullary hematopoiesis (EMH) is a rare condition encountered in chronic hemolytic disorders. Case report A 30-year-old man diagnosed as thalassemia intermedia since the age of 13 and receiving blood transfusion on demand was admitted to Kasr ELAini hospital because of back pain and weakness in both lower limbs that had progressed over the month before the admission with urinary precipitancy. He experienced similar condition 10 months before the current one with marked improvement after blood transfusion. On examination, he had characteristic mongoloid facies, pallor, and jaundice. After packed red cell transfusion, the patient condition markedly improved and he could walk without support
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