Abstract
Aim: To discuss the management of rare pediatric tumor, Gastrointestinal Stromal Tumor (GIST)Methods: We report a case of 1 year old male child with transverse colonic GIST. Child presented with upper abdominal lump of one month duration with no other constitutional symptoms. On examination solitary intra-abdominal lump of size 10cm and 8cm, non tender, firm, freely mobile in the umbilical region was found. Contrast enhanced CT abdomen revealed 8.3cm and 6.2cm heterogenous enhancing mass at root of the mesentery. On exploration an exophytic pedunculated mass was arising from mid transverse colon, tumor excised along with 2 cm colonic margin. Counselling done as chemotherapy was not available in children. Child has been under regular followup for the last 18 months. Results: Histopathological examination revealed GIST with high mitotic index, immuno-histochemistry (IHE) markers CD117,CD34 and DOG 1 were positive.Conclusion: Pediatric GIST is very rare and there are no well established therapeutic guidelines for the management of pediatric GIST, so needs close long term followup after surgery and further guidelines need to be established.
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