A rare case of double orifice mitral valve with flail leaflet with embryological significance  A case report

Gattu Praveen Kumar,Md Shaffiuddin

doi:10.3329/bjms.v13i1.17442

A rare case of double orifice mitral valve with flail leaflet with embryological significance A case report

Gattu Praveen Kumar, Md Shaffiuddin

Open Access

https://doi.org/10.3329/bjms.v13i1.17442

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Abstract

Mitral valve having a double orifice opening into the left ventricle is an uncommon anomaly, In this case study we describe about a 25 years old female who came to cardiology outpatient block with exertional dysnea , the abnormality was suspected by a murmur ,further investigation Colour Doppler echocardiography showed congenital double-orifice mitral valve. This finding was confirmed by open heart surgery, and her mitral valve was successfully repaired. DOI: http://dx.doi.org/10.3329/bjms.v13i1.17442 Bangladesh Journal of Medical Science Vol. 13 No. 01 January2014: 80-83

Highlights

The mitral orifice is well –defined transitional zone between the left atrium and left ventricle
Normal mitral valve consists of a central orifice located between anterior leaflet and posterior leaflet
Since the atrioventricular canal enlarges to the right, blood passing through the atrioventricular orifice has direct access to the primitive left as well as the primitive right ventricle

Summary

Introduction

The mitral orifice is well –defined transitional zone between the left atrium and left ventricle. At the end of the fourth week, two mesenchymal cushions, the atrioventricular endocardial cushions appear at the superior and inferior borders of the atrioventricular canal. The superior and inferior endocardial cushions, the two lateral atrioventricular cushions appear on the right and left borders of the canal. The superior and inferior cushions, in the meantime , project further into the lumen and fuse , resulting in a complete division of the canal into right and left atrioventricular orifices by the end of the fifth week. Muscular tissue in the cords degenerates and is replaced and id replaced by dense connective tissue, the valves consist of connective tissue covered by endocardium They are connected to thick trabeeculae in the wall of the ventricle, the papillary muscles, by means of chordate tendineae.

Double orifice mitral valve withflail leaflet with embryological significance

Findings

Discussion