Abstract
A 4 year-old male presented with effort dyspnea, and was diagnosed as atrioventricular canal defects. This finding was confirmed by open heart surgery, and a congenital double orifice mitral valve was discovered. The septal defect was closed but the double orifice mitral valve was respected because of the absence of hemodynamic disturbance. We report this case with review of literature.
Highlights
Double orifice mitral valve (DOMV) is a rare congenital malformation characterized by a mitral valve with two orifices
Rosenberg et al reported that 25% of patients with DOMV have partial persistent AV canal and about 5% of patients with partial persistent AV canal have DOMV [4]
Echocardiographic classification was proposed by Trowitsch et al, which divided DOMV into 3 different types: a: hole type, b: complete bridging, and c: incomplete bridging [6]
Summary
Double orifice mitral valve (DOMV) is a rare congenital malformation characterized by a mitral valve with two orifices. This anomaly is usually detected with other cardiac malformation [1]. Double orifice mitral valve may allow normal blood flow between the left atrium and LV, it can substantially obstruct mitral valve inflow or produce mitral valve incompetence [2]. Following is a case of DOMV; we have experienced with atrioventricular (AV) canal defects. Echocardiography provided a diagnosis of atrioventricular (AV) canal defects. The primumatrial septal defect (ASD) and the mitral cleft were seen. A congenital DOMV was fortuitously discovered (Figure 1). The primum ASD was closed by a patch and the mitral cleft was partially closed in the summit. The DOMV was respected because of the absence of hemodynamic disturbance (Figure 2)
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