A Congenital Pulmonary Airway Malformation (CPAM) Stocker’s Type III

Abstract

Congenital pulmonary airway malformation (CPAM) is a rare congenital abnormality that can manifest from prenatal period to childhood or uncommonly to adulthood. The diagnosis can be suspected from prenatal ultrasound, postnatal CT or MR imaging, however the mainstay of diagnosis is from histopathology. The rarest type of CPAM along with a poorer prognosis is Stocker’s type III, as it usually involves the entire lobe of the affected lung. We present a case of an infant with type III CPAM, which has difficulty in establishing the diagnosis initially, but later was managed appropriately and showed clinical improvement afterward.