A case report of desmoid tumor involving the head and neck region: challenges in diagnosis and treatment

Abstract

Desmoid tumor, or aggressive fibromatosis, is a rare condition affecting young adults. Diagnosis is challenging as it has to be established histopathologically by experienced oncopathological experts. Treatment options include surgery, radiation, and other forms of noninvasive modalities like hormonal therapy, low-dose and conventionaldose chemotherapy, non-steroidal anti-inflammatory drugs, tyrosine kinase inhibitors, etc. Each treatment modality has its own advantages and disadvantages. Also, there is a lack of clear guidelines for the management of such tumors, so the treatment-related decisions also become more challenging. Here, we are presenting such a case that was successfully treated using radiation alone with minimal side effects and achieved a good outcome in terms of tumor control, functional preservation, and cosmesis. Hopefully, it will help the medical community in deciding the treatment options and acting as a base for future studies.