A Case of Atypical Cystic Lymphangioma with Fatty Content

Abstract

Cystic lymphangioma is a congenital anomaly typically detected in early childhood. It predominantly affects the cervical region but can also manifest in other areas such as the mesentery, omentum, and retroperitoneum. Complications, influenced by the lesion's location and size, underscore the critical need for early diagnosis to prevent potential abdominal complications like mesenteric ischemia, volvulus, and bowel obstruction. While radiological imaging may raise suspicion, histological examination remains the definitive diagnostic approach. Treatment primarily involves surgical excision. Here, we present a case of an intra- and retroperitoneal cystic lesion with fatty content on CT and MRI, initially suggestive of either a modified cystic lymphangioma or a teratoma. Subsequent histopathological analysis confirmed the diagnosis of cystic lymphangioma.