Abstract
Patient history and physical: A 25-year-old African American female was admitted for painful oral erosions and widespread blistering lesions on the trunk and extremities which had been waxing and waning since age 12 years old. Disease flares requiring hospitalization had been continuing to occur multiple times annually in spite of numerous systemic immunosuppressive agents including chronic corticosteroids (resulting in Cushingoid features and insulin-dependent diabetes) in combination with cyclosporine, dapsone, tacrolimus, anakinra, rituximab, adalimumab, apremilast, mycophenolate mofetil, and intravenous immunoglobulin (IVIG) at various times.
Published Version
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