Клинический случай выраженной внутренней гидроцефалии при мальформации Денди-Уокера

Abstract

Dandy-Walker syndrome is a complex of symptoms presented by a congenital malformation involving essential structures of the brain: cerebellum, ventricles, medulla oblongata, cranial nerves and large vascular trunks, and characterized by especially severe course. In the article, a clinical case of pronounced internal hydrocephalus in Dandy-Walker malformation is described. Peculiarities of the given case are young age of the patient and diagnosis at the advanced stage when a stable neurologic deficit and alteration of the personality of organic type have already been formed. Thus, the performed neurosurgical intervention (endoscopic triventriculocisternostomy) appeared of low effectiveness and caused aggravation of the patient’s condition in the late postoperative period in the form of subdural hematoma which required a repeated operation for its removal. Conclusion. Issue of the internal hydrocephalus in Dandy-Walker syndrome is of much practical interest for both neurosurgeons, and neurologists and radiologists, since the modern diagnosis and effectiveness of treatment directly depend on the coordinated work of these specialists.