Stewart-Bluefarb Syndrome Research Articles

Acroangiodermatitis or pseudo-Kaposi’s sarcoma: a challenging diagnosis

Acroangiodermatitis (AAD), also referred to as pseudo-Kaposi’s sarcoma, is a vascular-proliferative disease characterized by reactive proliferation of small blood vessels in response to congenital or acquired vascular lesions. There are mainly two clinical variants of acroangiodermatitis; STEWART-BLUEFARB syndrome and the Malian type. There is clinical and histological similarity with Kaposi’s sarcoma hence the interest of immunohistochemical analysis. We report the case of a 40-year-old man with cutaneous lesions localized on the lower limbs. Clinical, dermoscopic, histological and immunohistochemical investigation led to a diagnosis of Kaposi-like acroangiodermatitis.

Recurrent Foot Ulcers in Young Woman: Stewart-Bluefarb Syndrome: Report of One Case and Literature Reviews

Stewart-Bluefarb syndrome (SBS) is one kind of the acroangiodermatitis, which is associated with an acquired or congenital arteriovenous malformation. This is a rare syndrome characterized by cutaneous lesions that usually onset at the second decade. We report the Stewart-Bluefarb syndrome in a 20-year-old woman presenting as recurrent foot ulcers of the right foot with multiple arteriovenous malformations. Diagnosis of SBS was confirmed histologically and radiologically. The clinical features of this disorder and the treatment options are reviewed.

Stewart-Bluefarb syndrome: A case report with angiographic findings

Acroangiodermatitis is a group of benign, angioproliferative cutaneous disease caused by chronic venous insufficiency, acquired or congenital arteriovenous shunts and limb paralysis. Stewart-Bluefarb syndrome is the type of acroangiodermatitis which is associated with a congenital arteriovenous malformation. This is a rare syndrome characterized by cutaneous kaposiform lesions that usually onset at the second decade. In this report, a case of acroangiodermatitis associated with a congenital arteriovenous malformation, which has been diagnosed after 40 years, is described.

Acroangiodermatitis Mali resulting from arteriovenous malformation: report of a case of Stewart–Bluefarb syndrome

We describe the rare Stewart-Bluefarb syndrome in a 15-year-old boy. This syndrome presents as a congenital arteriovenous malformation of the lower leg with multiple arteriovenous shunts accompanied by the benign acroangiodermatitis of Mali (pseudo-Kaposi's sarcoma). The clinical features of this disorder and the treatment options are reviewed.

Síndrome de Stewart-Bluefarb

Stewart–Bluefarb syndrome is a rare condition involving skin lesions that share clinical features with Kaposi sarcoma and that are secondary to an underlying arteriovenous fistula. We report the case of a 24-year-old man with progressive growth of skin lesions on the lower third of his left leg. Diagnosis of Stewart–Bluefarb syndrome was confirmed histologically and with detection of an arteriovenous fistula.

Ulcus bei AV-Fisteln im Rahmen eines Stewart-Bluefarb-Syndroms: Therapie der Arterien und/oder Venen?

We report on a 46-year old female patient with a 2-year history of ulceration over the dorsum of her right foot associated with a congenital arteriovenous fistula. About 12 years ago she had an ulcer at the same site. Despite an insufficient occlusion of the arteriovenous fistula after coil-embolization complete healing of the ulcer was achieved for a period of 10 years. At present hyperpigmentation could be seen surrounding the ulcer as a clinical sign for a venous insufficiency. The ulcer healed completely under a conservative therapy of the venous component of the arteriovenous fistula. The pathogenesis and therapy of ulcers associated with arteriovenous fistula within a Stewart-Bluefarb syndrome are discussed in this case report.

Stewart-Bluefarb Syndrome

Stewart—Bluefarb syndrome is a rare condition involving skin lesions that share clinical features with Kaposi sarcoma and that are secondary to an underlying arteriovenous fistula. We report the case of a 24-year-old man with progressive growth of skin lesions on the lower third of his left leg. Diagnosis of Stewart-Bluefarb syndrome was confirmed histologically and with detection of an arteriovenous fistula.

Kaposiform Acro-Angiodermatitis with Arteriovenous Malformation (Stewart-Bluefarb Syndrome)

A case of acro-angiodermatitis with congenital arteriovenous fistulae (Stewart-Bluefarb syndrome) at the distal right foot in a young man is reported. The lesion evolved slowly from a small dark-red spot existing from birth. Besides mechanical disturbances, the patient's only symptoms were a warmer and somewhat bigger right foot compared to the left nonaffected side. He presented a circumscribed spongy, livid-red coloured angiomatous lesion at the upper part of the distal right foot, also involving the proximal parts of the three middle toes. The diagnosis was based on the clinical aspect and the findings by Doppler ultrasonographic and oscillographic examination. The transcutaneous oxygen pressure showed a marked hypoxia at the edge of the acro-angiodermatitis. Finally, arteriovenous fistulae were demonstrated by arteriography.

Pseudo-angiosarcomatose de Kaposi sur membre paralytique

4 cases of acroangiodermatitis developing on paralytic feet are reported. Acroangiodermatitis might be an entity different from Mali's syndrome and Stewart-Bluefarb's syndrome. Paralysis could generate the dermatologic lesions by increasing venous stasis and enhancing arteriovenous channels.