You have accessJournal of UrologyCME1 Apr 2023V05-10 ROBOTIC BILATERAL PARTIAL ADRENALECTOMY FOR TREATMENT OF VON HIPPEL-LINDAU ASSOCIATED BILATERAL PHEOCHROMOCYTOMA Kassandra Dindinger-Hill, Kristen Pauley, Benjamin Maughan, Bogdana Schmidt, Brock O'Neil, Christopher Dechet, and Alejandro Sanchez Kassandra Dindinger-HillKassandra Dindinger-Hill More articles by this author , Kristen PauleyKristen Pauley More articles by this author , Benjamin MaughanBenjamin Maughan More articles by this author , Bogdana SchmidtBogdana Schmidt More articles by this author , Brock O'NeilBrock O'Neil More articles by this author , Christopher DechetChristopher Dechet More articles by this author , and Alejandro SanchezAlejandro Sanchez More articles by this author View All Author Informationhttps://doi.org/10.1097/JU.0000000000003263.10AboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail Abstract INTRODUCTION AND OBJECTIVE: Partial adrenalectomy is an essential approach for patients with von Hippel-Lindau (VHL) associated pheochromocytoma. One key benefit of partial adrenalectomy is avoidance of lifelong hormone replacement therapy. The purpose of this report is to demonstrate one case of robotic bilateral partial adrenalectomy for treatment of bilateral pheochromocytoma in a patient with VHL. METHODS: The patient was an 18-year-old male with a history of VHL diagnosed at birth who did not follow surveillance. The patient presented for hypertensive crisis leading to partial loss of vision in one eye, at which time plasma free metanephrines and normetanephrines were found to be significantly elevated. Patient was stabilized but continued to have persistent hypertension in the 130’s to 150’s systolic despite doxazosin and lisinopril therapy. Computed tomography (CT) of the abdomen and pelvis showed multiple bilateral large heterogeneously enhancing adrenal lesions consistent with bilateral pheochromocytomas (4 cm and 3 cm lesions on the right and 3.3 cm lesion on the left). The patient then underwent robotic bilateral partial adrenalectomy after adequate pre-operative adrenergic blockade. RESULTS: Robotic bilateral partial adrenalectomy was successfully performed with approximately 30% sparing of the adrenal glands bilaterally. Patient was hemodynamically stable with no post-operative complications. Pathology report showed complete excision of pheochromocytomas bilaterally. Patient has not required continued hydrocortisone replacement since time of surgery. CONCLUSIONS: This case demonstrates that bilateral partial adrenalectomy can be an effective management for bilateral pheochromocytoma to prevent the need for lifelong hormone replacement that would occur as a result of total adrenalectomy. Source of Funding: None © 2023 by American Urological Association Education and Research, Inc.FiguresReferencesRelatedDetails Volume 209Issue Supplement 4April 2023Page: e427 Advertisement Copyright & Permissions© 2023 by American Urological Association Education and Research, Inc.MetricsAuthor Information Kassandra Dindinger-Hill More articles by this author Kristen Pauley More articles by this author Benjamin Maughan More articles by this author Bogdana Schmidt More articles by this author Brock O'Neil More articles by this author Christopher Dechet More articles by this author Alejandro Sanchez More articles by this author Expand All Advertisement PDF downloadLoading ...