MNTI is a rare dysembryogenic tumor of infancy. It is a benign neoplasm usually seen in the first 6 months of life. The predominant site of origin is the pre-maxilla with rapid expansile growth manifesting with feeding difficulty. The tumor arises from the neural crest cells. On histological examination, typical biphasic population of cells with deposits of melanin pigment is seen. Immunohistochemistry (IHC) study helps in confirming the diagnosis. It has a locally aggressive course with high recurrence rate. Malignant transformation and metastatic spread is extremely rare. Wide excision of the tumor is the treatment. Thorough follow-up is recommended for a period of 1 year. Early detection and proper surgery decreases complications with favourable outcome. A case report of this tumor affecting a 5-month old male child with involvement of the right maxillary antrum is being presented here. This case is reported for its rarity, and classical clinico-pathological findings.