Partial Endocardial Cushion Defect Research Articles

Giant Partial Endocardial Cushion Defect Challenging Mitral Valve Replacement in Adults: Surgical Approach.

Atrial septal defect (ASD) is one of the most common congenital heart diseases diagnosed in children and adults [ [1] Steele P.M. Fuster V. Cohen M. Ritter D.G. McGoon D. Isolated atrial septal defect with pulmonary vascular obstructive disease – long-term follow-up and prediction of outcome after surgical correction. Circulation. 1987; 76: 1037-1042 Crossref PubMed Scopus (236) Google Scholar ]. Interventional closure devices or surgical patch closure are potential treatment options in haemodynamically relevant ASD. Concomitant severe mitral valve regurgitation is impeded by persisting type I ASD, as a congenital partial endocardial cushion defect (PECD) might be present. Partial endocardial cushion defect is a rare form of congenital heart failure, accounting for about 3% of the overall incidence [ [2] Robinson C.L. Merriman J.E. Kilduff C.J. Partial endocardial cushion defects. Can Med Assoc J. 1963; 88: 1147-1154 Google Scholar ].

Initial study of transthoracic echocardiography guided three-dimensional printing on the application of assessment of structural heart disease

Objective: To investigate the feasibility and diagnostic value of preoperative transthoracic echocardiography guided three dimensional printing model (TTE Guided 3DPM) on the assessment of structural heart disease (SHD). Methods: From February 2016 to October 2016, 44 patients underwent cardiac surgery in Tianjin Chest Hospital, forty-four patients were assessed preoperatively using TTE Guided 3DPM, including 25 males and 19 females, aged 3-75 years, with an average of (44±22) years. compared to conventional three dimensional transthoracic echocardiography (3D-TTE), and took direct intraoperative findings as "Golden Standard" simultaneously. There are twelve patients with SHD, including four cases with mitral prolapse, two cases with partial endocardial cushion defect, two cases with secondary atrial septal defect, two cases with rheumatic mitral stenosis, one case with tetralogy of Fallot, one case with ventricular septal defect (VSD), thirty-two patients without SHD were designed as negative control. Results: The sensitivity and specificity of TTE Guided 3DPM were greater than or equal to 3D-TTE, P value of McNemar test of 3D-TTE was greater than 0.05, the difference was not statistically significant, kappa=0.745, P<0.01, indicated that the results of 3DTTE and the gold standard were generally consistent.P value of McNemar test of TTE Guided 3DPM was greater than 0.05, the difference was not statistically significant, kappa=0.955, P<0.01, indicated that the results of TTE Guided 3DPM and gold standards were consistent. Compared with 3D-TTE and TTE Guided 3DPM, P value was greater than 0.05, the difference was not statistically significant, kappa=0.879, P<0.01, indicated that the results of 3D-TTE and TTE Guided 3DPM were consistent. TTE Guided 3DPM displayed the three-dimensional structure of SHD cardiac lesions clearly, which were consistent with intraoperative findings. Conclusion: TTE Guided 3DPM provides essential information for the preoperative evaluation and decision of SHD.

Partial endocardial cushion defect with Raghib's syndrome: a rare case report

Partial endocardial cushion defect with Raghib's syndrome: a rare case report

Comparison of clinical outcomes and postoperative recovery between two open heart surgeries: minimally invasive right subaxillary vertical thoracomy and traditional median sternotomy

ObjectiveTo compare the clinical outcomes of minimally invasive right subaxillary vertical thoracotomy and traditional median sternotomy through right atrium in treatment of common congenital heart diseases. MethodsClinical data of 59 cases of common congenital heart diseases treated with minimally invasive right axillary vertical thoracotomy from May, 2011 to February, 2013 and 77 cases of same diseases with traditional median sternotomy in the past three years were retrospectively analyzed, including atrial septal defect, membranous ventricular septal defect and partial endocardial cushion defect. The results were compared from the two groups, including the time for operation and cardiopulmonary bypass, amount of blood transfusion, postoperative drainage, ventilation time, hospital stay, and prognosis. ResultsNo severe complications happened in both groups, like deaths or secondary surgery caused by bleeding. No significant differences were in CPB time and postoperative ventilator time between groups (P>0.05), while for all of the operative time, the length of incision, postoperative drainage and hospital stay, minimally invasive right axillary vertical thoracotomy was superior to median sternotomy, with statistically significant differences (P<0.05). In six-month followup after operation, no complications of residual deformity and pericardial effusion were found in both groups by doing echocardiography, but mild pectus carinatum was found in 8 patients in the traditional median sternotomy group (traditional group), whereas patients in another group were well recovered. ConclusionsMinimally invasive right subaxillary vertical thoracotomy for common congenital heart diseases is as safe as traditional median sternotomy, without the increasing incidence of postoperative complications. Additionally, compared with traditional median sternotomy, minimally invasive right subaxillary vertical thoracotomy is better in the aspects of hidden incision, appearance, and postoperative recovery.

Partial endocardial cushion defect combined with persistent left superior vena cava to left atrial roof &amp; cor triatriatum in an adult patient

Methods and results We report here with a case corresponding to the above disease entity, in which pulmonary veins were drained into a separate posterior chamber, which was connected to the common atrium, thus forming cor triatriatum. A 42-yearold Asian female was consulted for operation of p-ECD and PLSVC, which were detected during the evaluation of complete heart block. She complained of worsening dyspnea and syncope attack for recent one year. The PLSVC had no connection with right sided SVC and was thought to be drained into the left atrial roof directly. The operation was carried out under standard hypothermic cardiopulmonary bypass. A large common atrium without septal remnant was encountered on opening right atrium. The coronary sinus opening was absent and PLSVC was directly drained into atrial roof, to the right of the left atrial appendage. An opening measuring 3x3cm, which at first was confused as atrial septal defect, was seen to the right of PLSVC. An accessory chamber, draining all four pulmonary veins was connected to the common atrium by this opening. After closing mitral valve cleft, a generous intraatrial patch made of bovine pericardium was used to partition the common atrium. The opening connecting pulmonary venous chamber to the atrium was widely extended inferiorly and the upper part of the opening was partly closed to minimize distortion of the patch. The left atrial appendage was also incorporated into the right side of patch to simplify the baffling procedure. The tricuspid annuoplasty was carried out and permanent epicardial pacemaker was implanted n the end. The patient recovered without events.

A Feline Case of Partial Endocardial Cushion Defect to Which Radical Surgery was Performed Using an Extracorporeal Circulation System

A Feline Case of Partial Endocardial Cushion Defect to Which Radical Surgery was Performed Using an Extracorporeal Circulation System

Left Main Coronary Artery Compression in Partial Endocardial Cushion Defect. Stent Implantation

Left Main Coronary Artery Compression in Partial Endocardial Cushion Defect. Stent Implantation

Sudden unexpected death in an adult patient with endocardial cushion defect

A 50-year-old male died following a road traffic accident. Postmortem examination revealed that the injuries caused by the accident did not seem to have caused his death. A large ostium primum defect was found, with bridging leaflets attached to the interventricular septum. In this article, we present a case of sudden death with partial endocardial cushion defect and discuss the mechanism of death. We believe that this is the first report of sudden death caused by endocardial cushion defect.

Port-access cardiac surgery. Experience with 34 cases at Keio University Hospital.

We reviewed our experience with port-access cardiac surgery and evaluated the medical effects and benefits of this technique in view of postoperative quality of life and medical expenses incurred during hospitalization. From June 1998 to August 2000, port-access cardiac surgery was conducted on 34 patients--22 with atrial septal defect, 6 with mitral regurgitation, 2 with coronary artery disease, 2 with partial endocardial cushion defect, 1 with ventricular septal defect, and 1 with atrial and ventricular septal defects. Two types of endoaortic-balloon catheters were used to execute aortic cross-clamping. Skin incisions were 5 cm long. No hospital or late deaths were observed. Patients with atrial septal defect were discharged on postoperative day 3.7, patients of mitral regurgitation on postoperative day 4.2, and patient of ventricular septal defect on postoperative day 4.0 on the average. None were readmitted. Patients appeared undisturbed by early discharge and were able to resume physical work on day 22 on the average after discharge. Patients undergoing port-access cardiac surgery recovered quickly from surgery and resumed work quickly. This technique thus proved satisfactory both physically and mentally to patients and improved their quality of life. Medically and economically this technique proved extremely beneficial. We confirmed it to constitute a viable approach and option for cardiac surgery in selected patients.

Partial Endocardial Cushion Defect with Aneurysm of the Anterior Mitral Leaflet in a 70‐Year‐Old

Mitral valve abnormalities are commonly associated with partial endocardial cushion defect. Aneurysm of the cleft leaflet has not been described in association with partial endocardial cushion defect. This case describes the aneurysmal deformity of the cleft leaflet in a 70‐year‐old woman diagnosed by transesophageal echocardiography imaging.