Multiple Impacted Supernumerary Teeth Research Articles

Cleidocranial dysplasia associated with dentigerous cyst-review of literature and case report of two siblings.

Cleidocranial dysplasia (CCD) is a developmental anomaly of the skeleton and teeth which may be inherited, be transmitted as dominant characteristics in either male or female or even appear spontaneously. A case was reported in the department of oral medicine and radiology of two sisters age 17 and 19 years old with a chief complaint of milk teeth not falling since childhood. They presented specific physical and oral findings in common which suggested the idea of an undiagnosed syndrome. The sisters showed CCD characteristics including short stature (4 feet) and frontal bone resorption indicating delayed closure of fontanels. The stature is moderately shortened with the neck appearing long and narrow and the shoulders markedly dropped. Dental abnormalities such as retention of primary dentition, multiple supernumerary teeth, and delayed eruption of permanent dentition. OPG showed the presence of multiple impacted permanent and supernumerary teeth with radiolucency involving the crowns of impacted teeth revealing a cystic lesion. Lateral cephalogram also revealed the presence of multiple impacted teeth. The provisional diagnosis of CCD with dentigerous cyst was given. The enucleation of cyst was done and submitted for histopathological examination. Histopathologically, the soft tissue section suggested the features of dentigerous cyst. The final diagnosis of CCD associated with dentigerous cyst was confirmed.

Surgical treatment of multiple impacted supernumerary teeth in a cleidocranial dysplasia patient

AbstractTo report a case of cleidocranial dysplasia (CCD) with 15 supernumerary teeth and review the relevant literature. Diagnose and treat a CCD patient with 15 impacted supernumerary teeth in the maxilla and mandible. When CCD is accompanied by supernumerary teeth ambushed in the jaw and does not affect the health of the body, it can be regarded as a part of normal bone tissue. If X‐ray or computed tomography examination shows that supernumerary teeth affect permanent tooth eruption, the replacement process of adjacent teeth and permanent tooth eruption should be closely observed, and supernumerary teeth should be extracted in time if necessary.

Fusion of multiple impacted supernumerary teeth with maxillary third molar - A rare case report

Fused supernumerary teeth are an uncommon finding. Fusion is an abnormality of tooth development. It is common in the lower anterior but rare in maxilla. Supernumerary teeth are additional teeth in normal series, occurring with a frequency of 0.3%–3.8% in population. The frequency of fusion of a permanent tooth with a supernumerary is <1% of cases and usually involves maxillary anterior teeth. Panoramic radiograph revealed a radiopaque mass in periapical region associated with maxillary third molar. The findings were suggestive of impacted supernumerary teeth. This case is an example of a rare phenomenon of fused multiple impacted supernumerary teeth in maxillary third molar area.

A MOUTH FULL OF TEETH: A CASE REPORT

<h3>Background</h3> An increase in the number of teeth is termed <i>supernumerary teeth</i>.¹^,² These teeth can be present both unilaterally or bilaterally, in one jaw, or in both jaws.² In the maxilla, the anterior region is the most common location, and a solitary tooth in the midline is referred to as <i>mesiodens</i>. However, supernumerary teeth are more often seen in the mandible, especially in the premolar region, and are referred to as <i>peridens</i>.¹^,² Supernumerary teeth distal to the molars are referred to as <i>distodens</i>.² This type of dental anomaly is commonly associated with developmental disorders, such as Gardner syndrome and cleidocranial dysplasia.²^,³ The excess number of teeth affects both the primary and permanent dentitions. It more commonly affects the permanent dentition and usually interferes with the eruption pattern, leading to malposition, crowding, ectopic eruption, and malocclusion.¹^,² <h3>Clinical and Radiographic Presentation</h3> A 9-year-old female with multiple impacted supernumerary teeth was referred by an orthodontist requesting a cone beam computed tomography (CBCT) scan for evaluation of impacted teeth. According to the clinic notes from the orthodontist, the patient was not complaining of any pain and had not been previously diagnosed with any medical disorder. There was no concerning medical history reported for the patient. The family history revealed that the patient's mother was deaf. The CBCT scan revealed multiple impacted permanent and supernumerary teeth in the jaws. On the basis of the radiologist's recommendation, the patient was referred to the University of Iowa Hospital and Clinic for genetic tests to rule out a possible underlying disorder. <h3>Differential Diagnosis</h3> Cleidocranial dysplasia, Gardner syndrome, Apert syndrome, and Crouzon syndrome were considered. <h3>Diagnosis and Management</h3> The CBCT scan revealed 19 impacted supernumerary teeth, apart from the impacted permanent teeth. The scan also showed a dentigerous cyst around the unerupted permanent mandibular right first molar. The image revealed multiple open sutures. A chest radiograph revealed marked variations in the clavicles bilaterally. On genetic testing, in addition to the findings from the scan, led to the diagnosis of cleidocranial dysplasia. The patient is currently scheduled for systematic removal of the supernumerary teeth as part of the comprehensive treatment plan. <h3>Discussion</h3> This case demonstrates the crucial role and importance of interpretation of CBCT volumes by a radiologist and the immense benefit of interdisciplinary care provided to a patient. CBCT is an excellent imaging tool to evaluate the location of teeth and aids in the treatment plan by revealing incidental findings that could be life changing for a patient and by enabling better patient care and outcomes.

Application of 3-D Imaging in a Familial Case of Cleidocranial Dysplasia

Cleidocranial dysplasia (CCD) is a rare inherited disorder affecting dental and skeletal tissues. CCD usually has an autosomal dominant pattern of inheritance and common clinical features seen are aplastic or hypoplastic clavicles, late closure of fontanelle, open skull sutures, retained deciduous teeth, late eruption of permanent teeth and presence of multiple impacted supernumerary teeth. Here, we present a case of CCD in a female patient with positive family history. The diagnosis was confirmed clinically and radiographically. The newer radiographic advancement, CBCT was used to validate the radiographic findings.

A Peculiar Case of Non-Syndromic Multiple Impacted Supernumerary Teeth- A Case Report with a total of 64 Teeth

A Peculiar Case of Non-Syndromic Multiple Impacted Supernumerary Teeth- A Case Report with a total of 64 Teeth

Dental phenotype of multiple impacted supernumerary teeth in Wiedemann–Steiner syndrome

Wiedemann–Steiner syndrome (WSS) is a rare autosomal dominant disorder characterized by short stature, intellectual disability, developmental delay, hypertrichosis cubiti, and dysmorphic facial features (thick eyebrows with a lateral flare, long eyelashes, vertically narrow and downslanting palpebral fissures, and wide nasal bridge). Dental findings reported with this syndrome are premature eruption of dentition, malocclusion, hypodontia, cleft palate, and retrognathia. We report a 12-year-old boy with a heterozygous two-base pair deletion in exon 22 of the KMT2A gene, resulting in a frameshift and premature truncation of the protein 17 amino acids downstream to codon 1974. Our patient exhibited multiple impacted supernumerary teeth which have never been reported earlier. This extends the dental phenotypic spectrum of WSS. To the best of our knowledge, this is the first reported case from India.

Main genetic entities associated with supernumerary teeth.

Supernumerary teeth represent a common human dental anomaly, defined as presence of extra teeth-more than the normal number foreseen in primary or permanent dentition. The prevalence has been reported between 0.2 to 3%, and is more frequent in males than females. The etiology is heterogeneous, highly variable and most of the cases are idiopathic. However, the presence of multiple impacted or erupted supernumerary teeth is rare and associated with some genetic syndromes: cleidocranial displasia, familial adenomatous polyposis, trichorhinophalangeal syndrome type I, Rubinstein-Taybi syndrome, Nance-Horan syndrome, Opitz G/BBB syndrome, oculofaciocardiodental syndrome and Robinow syndrome (autosomal dominant). The supernumerary teeth should be considered in order to possibly diagnose these entities with the aim of offering an interdisciplinary management and treatment, as well as offer adequate family genetic counseling.

Multiple Unerupted Impacted Supernumerary Teeth: A Rare Case Report of Father and Son

Multiple impacted supernumerary teeth without any associated systemic conditions or syndromes are rare. The prevalence rate of supernumerary teeth in the permanent dentition is between 0.1– 6.9 % as compared to 0.3–0.6% in theprimary dentition. In this article, reporting a rare family history of non-syndromic multiple impacted supernumerary teeth,found incidentally during routine radiographic examination. Though the etiologic factor of multiple impacted supernumerary teeth are still not clearly known especially in cases without any syndrome. However, thorough evaluation is necessary toexclude associated systemic conditions.

Multiple Impacted Permanent and Supernumerary Teeth in the Anterior Mandible of Nonsyndromic Case: A Systematic Review and Multidisciplinary Approach to Management

Multiple impacted permanent and supernumerary teeth have been associated with the syndromes and metabolic disorders. Approximately, 75% of all the supernumerary teeth are impacted and are asymptomatic. Consequently, most such teeth constitute casual findings in the context of routine X-ray studies. Lack of eruptive force and rotation of tooth buds may cause multiple impactions, and additional examinations may be necessary to exclude systemic and metabolic conditions. We present a rare nonsyndromic case with 11 multiple impacted teeth in the anterior mandible, with systematic literature review and multidisciplinary management.

Combined Orthodontic-surgical Treatment for Skeletal Class III Malocclusion with Multiple Impacted Permanent and Supernumerary Teeth: Case Report

In this report we describe a combined orthodontic and surgical treatment for a 14-year-old boy with severe skeletal class III deformity and dental problem. His upper posterior primary teeth in the left side were over-retained and 6 maxillary teeth (bilateral central incisors and canines, left first and second premolars) were impacted, together with 5 supernumerary teeth in both arches. The treatment protocol involved extraction of all the supernumerary and deciduous teeth, surgical exposure and orthodontic traction of the impacted teeth, a bimaxillary orthognathic approach including Lefort I osteotomy. Bilateral sagittal split ramus osteotomy (BSSRO) and genioplasty was performed to correct skeletal problem. After treatment, all of the impacted teeth were brought to proper alignment in the maxillary arch. A satisfied profile and good posterior occlusion was achieved. Treatment mechanics and consideration during different stages are discussed.

Cleidocranial dysplasia presenting with retained deciduous teeth and impacted permanent and supernumerary teeth

Cleidocranial dysplasia is a disease that occurs secondary to a dominant autosomal inheritance. There is no predilection for any genre or ethnic group. As there is a delay in the eruption and/or absence of permanent teeth, the patients usually report to a dental surgeon for replacement of the missing teeth. This condition is characterized by several cranial malformations and underdevelopment, absence of clavicles, and multiple impacted supernumerary and permanent teeth. The diagnosis of the condition is usually based on the presence of the above-mentioned main features and on clinical and familial evidence. Here we report a rare case of cleidocranial dysplasia in a male patient, having most of the characteristic features of this syndrome.

Non-syndromic multiple impacted supernumerary teeth: two case reports

Multiple impacted teeth may be related to syndromes and metabolic disorders. In some cases, however, impaction of multiple teeth is not accompanied by any other disorder or syndrom. Hyperdontia or supernumerary teeth without associated syndromes is a rare phenomenon, as supernumerary teeth are usually associated with cleft lip and palate or other syndromes such as Gardeners syndrome, cleidocranial dysplasia and trichorhinophalangic syndrome. The aim of this paper is to demonstrate that asymptomatic multiple impacted ectopic teeth are not always associated with a syndrome or a disorder. A 15-year old male patient attended our clinic with a chief complaint of irregular teeth and unaesthetic smile. In intraoral examination irregular and amorphous erupted teeth were noticed. On routine radiographical examination, impacted supernumerary teeth were noticed in maxilla and mandible. A 37-year old male patient attended our clinic for routine examination and radiographic examination revealed supernumerary and amorphous teeth in mandible and maxilla. In our cases, medical and family history and extraoral examination were not suggestive of any syndrome or metabolic disorder. A general physician was consulted who confirmed that there was no associated syndrome. The supernumarary teeth were surgically extracted. The 15 year old patient who was suffering from irregular teeth was directed to orthodontics clinic. In conclusion, routine radiographic examination may reveal multiple impactions, even if there is no absence of teeth. The etiologic factor of multiple impacted supernumerary teeth is still not clearly known, especially in cases without any syndrome. However, additional examinations may be necessary to exclude systemic and metabolic conditions.

A Rare Combination of Aggressive Periodontitis with Multiple Impacted Supernumerary Teeth

A Rare Combination of Aggressive Periodontitis with Multiple Impacted Supernumerary Teeth

多数の埋伏過剰歯を伴った鎖骨頭蓋異骨症の1例-3D-CTの有用性-

多数の埋伏過剰歯を伴った鎖骨頭蓋異骨症の1例-3D-CTの有用性-

Imaging in the diagnosis of a rare anomaly: Cleidocranial dysplasia

Cleidocranial dysplasia (CCD) is a rare autosomal dominant and developmental anomaly of skeleton characterized by generalized dysplasia of the bones and teeth. CCD is caused by mutation of transcription factor RuNx2, although 40% of the cases appear spontaneously with no apparent genetic cause. The disorder presents with partial or complete absence of clavicles, open anterior fontanelle, and cranial sutures, presence of multiple wormian bones, short stature, wide pubic symphysis, short middle phalanges of the 5 th finger, over retained deciduous teeth, multiple impacted permanent and supernumerary teeth and various other abnormalities. The frequency of this disorder is one/million individuals. Early diagnosis of CCD is essential for initiating the appropriate treatment approach. In confirmed cases, genetic counseling for family planning should certainly be advised. Because of its rarity, we report the classical case of CCD, with an emphasis on the importance of clinical and radiographic findings.

Clinical and radiological manifestations of cleidocranial dysplasia: A case report

Cleidocranial dysplasia is a rare hereditary disorder affecting bones and teeth. It can be inherited or can arise spontaneously. It is usually caused by a mutation in the Runx2 gene located on 6p21 chromosome. CCD is associated with complete absence or hypoplasia of the clavicles, delayed or deficient closure of the fontanellas and open sutures, retarded exfoliation of the deciduous teeth, retarded eruption of the permanent teeth and multiple impacted supernumerary teeth. Clinical and radiographic examination display abnormalities of bone and teeth. The main aim of this study is to discuss the diagnostic tools, clinical and genetic features of this disorder and review the literature. Radiographs of skull, teeth, clavicle and pelvis were the diagnostic evidences of our case.

An unusual presentation of generalized aggressive periodontitis with multiple impacted supernumerary teeth

Aggressive periodontitis is a rare condition that progresses rapidly but affects only a small percentage of population. Most of the cases are familial. The presence of supernumerary teeth is also rather rare and often familial. Therefore, a concomitant presentation of aggressive periodontitis and supernumerary teeth in an individual has generated a great interest among clinicians. Here, we report a rare nonsyndromic case of generalized aggressive periodontitis with multiple impacted supernumerary teeth.

Regional odontodysplasia—an unusual case occurring along with supernumerary teeth

Regional odontodysplasia (RO) is an unusual developmental anomaly which affects the ectodermal and mesodermal component in a group of contiguous teeth. Supernumerary teeth are those that are found in addition to the normal series of teeth. An interesting case of RO, multiple impacted supernumerary teeth and alveolar swelling in the second quadrant is reported here. Unlike the earlier reported cases, the case was unique in that the roots of the hypoplastic teeth showed continued root formation suggesting for more conservative treatment and no cases of simultaneous occurrence of RO and impacted supernumerary teeth have been reported in the literature.

Pyknodysostosis: report of a rare case with review of literature

Pyknodysostosis is a rare autosomal recessive disorder characterized by the post natal onset of short limbs, short stature, and generalized hyperostosis along with acro-osteolysis with sclerosis of the terminal phalanges, a feature that is considered essentially pathognomonic. Other features include persistence of fontanelles, delayed closure of sutures, wormian bones, absence of frontal sinuses, and obtuse mandibular gonial angle with relative mandibular prognathism. We report a case of 17-year-old girl who presented with a chief complaint of retention of deciduous teeth. General physical examination demonstrated short stature, frontal and parietal bossing, depressed nasal bridge, beaked nose, hypoplastic midface, wrinkled skin over the finger tips, and nail abnormalities. Radiographs showed multiple impacted permanent and supernumerary teeth, hypoplastic paranasal sinuses with acro-osteolysis of terminal phalanges, and open fontanelles, and sutures along with wormian bones in the lambdoidal region.