AbstractMucinous cystic neoplasms of the liver (MCN-L) are a rare benign neoplasm of the biliary system that grows slowly with vague clinical symptoms. The malignant transformation in these tumors is high, and preoperative diagnosis using radiography or endoscopy is challenging. We present a case report of a 58-year-old female patient who presented with diffuse abdominal pain and nonprojectile vomiting. Abdominal ultrasound revealed characteristics that point to a hydatid cyst. The enhanced computed tomography revealed a well-defined multiloculated thin-walled fluid density lesion in the left lobe of the liver. After a left hemi-hepatectomy, a multiloculated cystic lesion in the liver with mucinous material as the content was discovered. Histopathology showed multiple cystic spaces were lined by mucin-secreting columnar epithelium without nuclear atypia, the wall of the cysts showed ovarian-like stroma, and the diagnosis of MCN-L was made. There was no recurrence after 6 months of regular follow-up.