Fibrous Dysplasia Of Maxilla Research Articles

Fibrous Dysplasia of Maxilla in a 10 Year Old Boy

Fibrous Dysplasia of Maxilla in a 10 Year Old Boy

Fibrous Dysplasia Of Maxilla: A Case Report

Summary: Fibrous dysplasia is a benign disease of unclear aetiology that is congenital and recurring in nature. It is caused by a problem known as bone modelling, in which the normal bone constantly changes and is replaced by immature fibrous tissue. One or more bones may be impacted by the lesion; the maxilla is the most often afflicted facial bone. Expansile lesions known as fibrous dysplasia lead to issues related to the original location. The most often involved region in the craniofacial bone is the maxilla. In this case report 50 years 50-year-old female patient reported who has maxillary fibrous dysplasia. Keywords: fibrous dysplasia, congenital, bone.

Fibrous Dysplasia of Maxilla in a 5-year-old Child: A Rare Pediatric Case Report and Literature Review

Fibrous dysplasia (FD) is a rare benign fibro-osseous, nonhereditary skeletal disorder that results from the postzygotic mutation in the GNAS1 gene (20q13.2). It manifests variable clinical manifestations, namely monostotic, polyostotic, and craniofacial forms/types and may also constitute few syndromes. Updated scientific literature with case report articles about FD is utmost important for the awareness of the medical and dental clinicians to identify accurately and also to make individualized treatment plans with multidisciplinary approach. Hence, this current article presents and illustrates the case report about monostotic FD of the maxilla in a 5-year-old boy. Furthermore, the case findings have been correlated with the updated relevant literature.

Fibrous dysplasia of maxilla – A rare case report

Fibrous dysplasia (FD) is a skeletal developmental anomaly, which is non-hereditary in origin and idiopathic in nature. It is a benign fibro-osseous disease that affects one or more bones. It usually affects unilaterally and is seen in the posterior region. Approximately 0.5% of untreated cases show the malignant transformation. We report the case of a 35-year-old female patient with FD involving the maxilla. The clinical diagnostic approach, different imaging modalities, and histological examination methods for definitive diagnosis have been elaborated.

Application of 3D computer-assisted printing technique combined with plastic titanium mesh in the reconstruction of maxillary defect

Objective: To investigate the application and clinical outcomes of using 3D computer-assisted printing technique combined with plastic titanium mesh in the reconstruction of maxillary defect. Methods: Clinical data of 14 patients in Department of Otorhinolaryngology Head and Neck Surgery, Shanghai Ninth People's Hospital from January 2016 to June 2018, who were treated for partial or total removal of the maxilla due to benign or malignant tumors and those acquired maxillary defects caused by severe compound trauma were analyzed retrospectively. Twelve males and 2 females were included, with the age ranging from 16 to 51 years old. The sinonasal malignant tumors included squamous carcinoma (n=2) while benign tumors included hemangioma (n=1), maxillary fibrous dysplasia (n=3), maxillary cyst (n=2) and giant cell tumor of the maxilla (n=1). Five cases of post-traumatic maxillary defect were also included. According to preoperative thin-layer CT scanning data, computer modeling data was transmitted to a 3D printer to print out the original model and the reconstructed model. Preoperative simulation of tumor removal and maxillary reconstruction was done on the patient's original model, and the titanium mesh was shaped on the reconstructed model in order to properly reconstruct the area needed to be repaired. The pre-made titanium mesh was implanted into the defect area, the soft tissue flaps were reset, layered stitching and the local pressured bandage were used after surgery. Through postoperative clinical and CT examination, the patient's maxillofacial shape, nasal function and complications were evaluated. The results were analyzed by descriptive statistical method. Results: Lesions could be completely removed within the predicted range on the preoperative 3D-printed models of all cases. After debridement, titanium mesh could be implanted easily without re-shaping and trimming during surgery as in trauma cases. Titanium mesh could completely cover the missing bone surface closely, with titanium nails fixed smoothly, and the implanted titanium mesh was solid and stable. After the follow-up of 6 to 20 months, all patients were satisfied with the facial symmetry and the function was recovered well. Conclusion: Using 3D computer-assisted printing technique combined with plastic titanium mesh in the reconstruction of maxillary defect can accurately restore the maxillary structure for soft tissue support, and restore the facial shape and function.

Midfacial degloving approach for management of the maxillary fibrous dysplasia: a case report

BackgroundFibrous dysplasia (FD) is a benign bone lesion characterized by the progressive replacement of normal bone with fibro-osseous connective tissue. The maxilla is the most commonly affected area of facial bone, resulting in facial asymmetry and functional disorders. Surgery is an effective management option and involves removing the diseased bone via an intraoral approach: conservative bone shaving or radical excision and reconstruction.Case presentationThis case report describes a monostotic fibrous dysplasia in which the patient’s right midface had a prominent appearance. The asymmetric maxillary area was surgically recontoured via the midfacial degloving approach under general anesthesia. Follow-up photography and radiographic imaging after surgery showed the structures were in a stable state without recurrence of the FD lesion. Furthermore, there were no visible scars or functional disability, and the patient reported no postoperative discomfort.ConclusionsIn conclusion, the midfacial degloving approach for treatment of maxillary fibrous dysplasia is a reliable and successful treatment option. Without visible scars and virtually free of postoperative functional disability, this approach offers good exposure of the middle third of the face for treatment of maxillary fibrous dysplasia with excellent cosmetic outcomes.

A case of maxillary fibrous dysplasia treated by surgery using a navigation system

A case of maxillary fibrous dysplasia treated by surgery using a navigation system

Maxillary Fibrous Dysplasia with Cone Beam Computed Tomography Findings: A Case Report

Maxillary Fibrous Dysplasia with Cone Beam Computed Tomography Findings: A Case Report

Fibrous Dysplasia of Maxilla - Surgical Sculpting for Aesthetics

Fibrous Dysplasia of Maxilla - Surgical Sculpting for Aesthetics

Monostotic Type of Fibrous Dysplasia of Maxilla

Monostotic Type of Fibrous Dysplasia of Maxilla

Fibrous dysplasia of maxilla: An unusual case report

Fibrous dysplasia of maxilla: An unusual case report

Fibrous dysplasia of maxilla: A case report

Fibrous dysplasia of maxilla: A case report

Maxillary fibrous dysplasia associated with McCune-Albright syndrome. A case study.

McCune Albright syndrome (MCA) is a rare complication of genetic origin. The authors present a case study of a patient with MCA diagnosed with multifocal fibrous dysplasia in his limb and craniofacial bones. The symptoms of the disease in the patient’s facial and oral tissue and the treatment administered have been described.

Fibrous dysplasia of maxilla: Report of two cases

Fibrous dysplasia (FD) is an idiopathic skeletal disorder in which the trabecular bone is replaced and distorted by poorly organized, structurally unsound fibro-osseous tissue. The lesion is classified into two forms: Monostotic (75-80%) and polyostotic. A distinct form of Polyostotic FD, known as McCune-Albright Syndrome, is accompanied by cutaneous pigmentation and sexual precocity, and this occurs almost exclusively in women. Typical radiographic appearance shows an expanded osseous lesion having poorly defined margins covered by a thin eggshell cortex and lacking periosteal new bone formation. Here, we are presenting two case reports of FD involving the maxilla.

Fibrous dysplasia as a rare cause of nasolacrimal duct obstruction

Fibrous dysplasia of the paranasal sinuses is mostly asymptomatic, but sometimes may cause signs and symptoms de- pending on its location. We report two cases of maxillary fibrous dysplasia obstructing the lacrimal drainage system as a reason of chronic dacryocystitis, and reviewed the related literature. The first case underwent an endonasal endoscopic approach combined with external dacryocystorhinostomy. He had a patent lacrimal system at one-year follow-up. The le- sion was completely removed via an endonasal endoscopic approach in the second case, wherein the patient was asymp- tomatic of the six-month follow-up period.

Oral Rehabilitation With Dental Implants for Teeth Involved in a Maxillary Fibrous Dysplasia

Introduction: Fibrous dysplasia (FD) is a rare but important benign lesion affecting the maxillofacial region that presents bone pain, deformities, and fracture. Although FD presents radiographic patterns, it has to be analyzed histologically for a final diagnosis. Currently, there is no universally accepted guide for FD treatment. This case report describes a successful case of excision of the entire lesion in the upper left maxilla and the placement of two dental implants for oral rehabilitation, followed by guided bone regeneration.Case Presentation: A 49‐year‐old female patient presented with a growth on the left side of the maxilla that developed 4 years previously. Cone‐beam computed tomography was used to analyze the lesion and clinical features, and the FD was confirmed by histologic analysis. Extraction of the teeth involved with the lesion and excising the lesion was suggested. This was followed by two‐implant placement for oral rehabilitation, grafting the cavity with an osteoconductive material. Both implants were successfully integrated, as confirmed by clinical examination and a resonance frequency test.Conclusion: Dental implant and related guided bone regeneration can be successfully obtained in a patient with an FD lesion.

Midfacial Degloving Approach for Resectioning and Reconstruction of Extensive Maxillary Fibrous Dysplasia

The traditional unilateral or bilateral buccogingival or bicoronal approach often seems to impose limitations on achieving complete resection and reconstruction of the extensive midfacial fibrous dysplasia. Therefore, we hypothesized that the midfacial degloving approach could be used for the correction of maxillary fibrous dysplasia, which has been primarily used for paranasal sinus lesions or nasopharyngeal tumor. The study involved 5 maxillofacial fibrous dysplasia patients who underwent a midfacial degloving surgical procedure. There were 4 male patients and 1 female patient with a mean age of 16.8 years. The average, mean follow-up duration was 17.8 months. A wide, subperiosteal dissection was made along the anterior wall of the maxilla and pyriform aperture over the level of the infraorbital foramen. A bilateral, circumferential, nasal vestibular incision and dissection allowed for bilateral degloving of the middle third of the face over the infraorbital rim. Then total or subtotal resection, followed by reconstruction using an iliac bone graft, was performed. The midface, degloving approach provided visualization of the medial maxillary wall, the pterygoid junction, nasofrontal suture, infraorbital rim, and laterally to the temporal process of the zygoma. Subtotal or total resection of the lesions and reconstruction with bone grafts was possible in all 5 patients, and there were no complications. There was also no visible facial scarring and all patients expressed satisfaction with the cosmetic outcome. The midfacial, degloving approach was found to be safe and effective for maxillofacial fibrous dysplasia, and nearly total resection was possible. This approach allows for a wider dissection and resection compared with the traditional buccogingival approaches, and there was no visible facial scarring.

Distinctive Genital Folliculosebaceous Cystic Hamartomas in a Patient With Fibrous Dysplasia

Folliculosebaceous cystic hamartoma is a benign tumor composed of follicular, sebaceous, and mesenchymal components. Usually, it appears in adulthood as a dome or a pedunculated nodule on the face, especially the nose. Extracephalic lesions are sporadically reported, such as on the upper back, forearm, ear, labia majora, and the nipple. Herein, we report a patient with left maxillary fibrous dysplasia who experienced bilateral labia majora disfigurement after her puberty. She experienced physical distress because of tenderness due to the tangled, stretched hamartomas and psychological distress because of failure to have sexual contacts. The exophytic dark skin-colored fusing polypoid labia majora deformities were excised, and the folliculosebaceous cystic hamartoma was impressed by the pathology. We used an advancing flap for labiaplasty, and the outcome was aesthetically satisfactory. There is no recurrence in the 6-month follow-up period. To our knowledge, this is the first report of a folliculosebaceous cystic hamartoma on the bilateral labia majora in a patient with fibrous dysplasia. This extraordinary presentation is much different from others owing to its unusual appearance and a larger size.

Monofocal maxillary fibrous dysplasia with orbital, nasal and oral obstruction

Fibrous dysplasia is a condition characterised by excessive proliferation of bone-forming mesenchymal cells. Although a variety of causative factors are described, the exact aetiology is yet to be fully known. The maxilla is the most commonly affected facial bone, with facial asymmetry being the usual complaint. Surgery is the treatment of choice with two available options, namely, conservative bone shaving and radical excision and reconstruction. We describe the case of a 25-year-old male who presented with a giant monofocal fibrous dysplasia of the left maxilla with facial asymmetry, including obstruction of the left orbit, nasal and left half of the oral cavities and was treated with conservative surgery.

Reverse facial artery–submental artery mandibular osteomuscular flap for the reconstruction of maxillary defects following the removal of benign tumors

Functional and aesthetic restoration in maxillary reconstruction remains a challenge. Although many free flap procedures have become popular in maxillary reconstruction, these microsurgical methods have certain limitations and risks. This study assessed the reliability of the reverse facial artery-submental artery mandibular osteomuscular flap for reconstructing maxillary defects. Eight maxillary defects following benign tumor ablation were repaired with reverse facial artery-submental artery mandibular osteomuscular flaps. The patients ranged in age from 16 to 33 years; 5 were male and 3 were female. Maxillary odontogenic myxoma was present in 3 cases, maxillary fibrous dysplasia and ameloblastoma in 2 cases each, and chondromyxoid fibroma in 1 case. The defects were classified as class 2a. Primary reconstruction of the maxilla was carried out using a pedicled mandibular osteomuscular flap. No flap failures occurred. Dental reconstruction was successful in all patients. Proper aesthetics and complete functionality were obtained, and there were no donor-site problems. The patients were followed for 12 to 24 months, with an average of 18.6 months, and no recurrence was encountered. The reverse facial artery-submental artery mandibular osteomuscular flap is safe, quick, and simple to elevate. The flap can be used reliably for reconstructing maxillary defects.