Maxillary Duplication Research Articles

Bilateral Maxillary Duplication in Tessier No. 7 Cleft: An Uncommon Congenital Deformity with a Challenging Radiological Diagnosis.

Tessier No. 7 cleft, known as lateral facial cleft, is a rare and understudied entity with an incidence of 1/80,000-1/300,000 live births. Besides perioral tissue abnormalities manifesting as macrostomia, Tessier 7 cleft also involves anomalies of the underlying bony structures. It can appear as part of a syndrome, such as Treacher-Collins syndrome or Goldenhar/Orbito-Auriculo-Vestibular Spectrum, or as an isolated form (unilateral or bilateral) with variable expressions. Bilateral maxillary duplication in Tessier 7 cleft is considered extremely rare, accounting for only two previously presented cases. Given that the cases presented in the literature mainly focus on clinical appearance and surgical treatment, without providing sufficient imaging, we aim to present key radiological features of Tessier 7 cleft in terms of evaluating the involved structures, which is essential for the therapeutic approach and final outcome. A 17-year-old male with incompetent lips and orthodontic abnormalities was referred to our Radiology Department for orthopantomography (OPG) and CT examinations. Hetero-anamnestic data revealed a history of surgical treatment of the commissural cleft conducted 2 months after the birth to enable feeding. Intraoral examination showed a maxillary cleft and supernumerary teeth. Since the given clinical presentation was inconclusive, radiological diagnostics took precedence in elucidating this complex entity.

Congenital Tessier Type 7 Bilateral Maxillary Duplication: A Rare Craniofacial Deformity

It is uncommon for these rare congenital abnormalities to manifest as craniofacial clefts. The Tessier clefting scheme is one classification technique that is used for diagnosis. A maxillary duplication is an extra bone that is situated behind the maxillary tuberosity. The case of a six-year-old child with bilaterally supernumerary teeth who presented to the Department of Radiodiagnosis of our institute to assess and treat enlarged asymptomatic cheek swelling is presented. On the basis of the patient's medical history, physical examination, and radiological tests, the accessory maxillae were diagnosed. Later, there was a surgical reconstruction.

Duplication faciale partielle (un diprosope rare) : à propos d’un cas et revue de littérature

Diprosopus, or partial facial duplication, is a very rare congenital abnormality. It is a rare form of conjoined twins. Partial facial duplication may be symmetric or not and may involve the nose, the maxilla, the mandible, the palate, the tongue and the mouth. A male newborn springing from inbred parents was admitted at his first day of life for facial deformity. He presented with hypertelorism, 2 eyes, a tendency to nose duplication (flatted large nose, 2 columellae, 2 lateral nostrils separated in the midline by a third deformed hole), two mouths and a duplicated maxilla. Laboratory tests were normal. The cranio-facial CT confirmed the maxillary duplication. This type of cranio-facial duplication is a rare entity with about 35 reported cases in the literature. Our patient was similar to a rare case of living diprosopus reported by Stiehm in 1972. Diprosopus is often associated with abnormalities of the gastrointestinal tract, the central nervous system, the cardiovascular and respiratory systems and with a high incidence of cleft lip and palate. Surgical treatment consists in the resection of the duplicated components.

Journey to chew: A case of maxillary duplication and bony syngnathia

Tessier no 3 cleft, bony syngnathia, and maxillary duplication are rare as independent anomalies and have never been reported together in a single case. Here we present a patient with congenital bony syngnathia, maxillary duplication, and a Tessier no. 3 nasal cleft. Other abnormalities included situs inversus, dextrocardia, coarctation of the aorta, left choanal stenosis, left coloboma, and hypertelorbitism. Given the unique presentation, we present our early surgical management to this complex problem.

Congenital parotid ectopia in accessory maxilla and facial cleft anomalies: Three cases report

To further document the clinical features of accessory maxilla with three additional cases report. Clinical and radiological features of three cases of accessory maxilla were presented. Related literature was summarized for comparison. Ectopic parotid gland, facial cleft and accessory maxilla are three concomitant malformations in this condition. The tooth-bearing accessory maxillary duplication derives from the abnormal growth of the zygoma or zygomatic arch. Facial cleft, parotid ectopia and tooth-bearing accessory maxilla may constitute a rare congenital syndrome.

Accessory maxilla with a lateral cleft lip: A rare case report

Maxillary duplication is a rare congenital anomaly that occurs in the jaw/mouth region. Duplication of jaws carrying teeth may occur either as an accessory process or, more rarely, a complete jaw. The lateral cleft lip and accessory maxilla are rare congenital abnormalities likely to occur independently but this combined manifestation of accessory jaw processes and transverse facial clefts is exceedingly rare.We report an extremely rare case of accessory maxilla carrying teeth associated with a lateral cleft lip in a 17-year-old male along with a discussion on the pathogenesis, treatment protocol and the differential diagnosis with review of literature.

Bilateral maxillary duplication: case report and literature review

Accessory maxillary jaws are extremely rare occurrences. Currently, there is only 1 report of bilateral accessory maxillary jaws in the English-language literature. We present a case of a 7-year-old girl with bilateral bony exostoses extending from the maxillary tuberosities. The patient also had restricted protrusive and lateral excursive movements of the mandible. The histologic report revealed teeth in various developmental stages within the bony exostoses. We concluded that these structures were an isolated form of bilateral accessory maxillary jaws.

A case of maxillary duplication with a soft palate reconstruction using a forearm flap

Maxillary duplication is a rare congenital anomaly that occurs in the jaw/mouth area. It is generally regarded as sporadic in nature. Total or subtotal soft palate reconstruction for oropharyngeal defects, which include post-surgical and congenital defects, presents a difficult surgical challenge. A maxillary duplication in which the soft palate is reconstructed using a vascularized forearm flap is described. The velopharyngeal insufficiency in the present case is caused by the almost complete deficiency of the soft palate, suggesting that a conventional pharyngeal flap operation with localized mucosal myocutaneous flaps would not produce favorable results in terms of postoperative contractions in the pharyngeal flaps. In such cases, the reconstruction of the soft palate using vascularized free forearm flaps, guided by flexibility regarding the size and adequate thickness of the flaps, may be useful.

Neurocristopathy that manifests right facial cleft and right maxillary duplication

A case of 17-year-old girl with a right facial cleft and maxillary duplication is presented. A vascularized outer-table calvarial bone flap is used for the reconstruction of the bony defects as a result of an oblique facial cleft. The classifications of oblique facial clefts and treatment techniques are also discussed.

A case of neurocristopathy that manifests facial clefting and maxillary duplication

A case of a 6-year-old child with three facial clefts and maxillary duplication is presented. Computerized three-dimensional reconstruction from computerized tomography imaging was used in the diagnosis of this patient, and an explanation of the possible embryologic causes of this malformation is discussed.