Intra-abdominal Extralobar Pulmonary Sequestration Research Articles

Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration: a 12-year 3-center experience in China

To provide useful information for diagnosing and predicting fetal intraabdominal extralobar pulmonary sequestration (IEPS), a retrospective review of diagnostic approaches was conducted. Ultrasonography was performed serially in 21 fetuses with IEPS from 2005 to 2017. Prenatal sonographic features, treatment, and outcomes of each case were evaluated and collected. These cases of IEPS were also compared to 43 cases previously reported by other researchers from 1986 to 2017. Of the 21 sonographic features, 14 (67%) were hyperechoic, 21 (100%) were well circumscribed, and 17 (81%) depicted a mass that shifted with fetal breaths/hiccups non-synchronized with adjacent organs (sliding sign). Feeding arteries were detected prenatally in 18 patients (86%). The lesion volume was 10.17 ± 4.66 cm3, the congenital cystic adenomatoid malformation volume ratio and cardiothoracic ratio were in normal range. The gestational age at diagnosis, location and echotexture of the lesion, and rate of surgical treatment were similar to previous studies, but with a significantly higher rate of detected feeding arteries (P < 0.01), and associated anomalies (P < 0.01). All infants who underwent surgery after birth had satisfactory outcomes. The sliding sign and feeding artery are essential features of IEPS in prenatal diagnosis.

A Case of Intra - Abdominal Extralobar Pulmonary Sequestration: Prenatal Detection, Postnatal Diagnostic Approach and Outcome

This paper describes the perinatal and postnatal outcome of a case considered to have a fetal intra-abdominal extralobar pulmonary sequestration (ELS). Routine midtrimester fetal ultrasonographic scan detected an abdominal echogenic mass between aorta and stomach. It was considered primarily as an intra-abdominal ELS. At postnatal 2 months, computed tomography (CT) scan with intravenous contrast described it as an ELS at the level of diaphragmatic hiatus by showing the aberrant blood supply to the sequestration with venous drainage into the portal confluence. The patient is now 4 years old and asymptomatic; she is being followed-up by a pediatric surgeon. Intra-abdominal ELSs usually remain asymptomatic throughout life; they may be safely observed without surgery unless they become symptomatic or show any change in the characteristics of the radiologic appearance.

Prenatal diagnosis of intraabdominal extralobar pulmonary sequestration by ultrasound

Objective To describe the diagnostic approach and clinical outcomes of fetal intraabdominal extralobar pulmonary sequestration (IEPS). Methods Three cases of IEPS were diagnosed prenatally by ultrasound in our center. The data of these 3 cases and 43 cases in prior studies from 1986 to 2016 were retrospectively reviewed. The prenatal sonographic features, treatment, and outcomes were collected. Results The gestational age of diagnosis IEPS was (24.5±5.9)weeks, the male-to-female ratio was 3-4∶1, 78.3% (36/46) of IEPS masses located on the left side, 47.8% (22/46) of lesions were homogenous and hyperechoic, 8.7% (4/46) of cases associated anomalies, 78.3% (36/46) of patients were preformed resection and postoperative recovery and subsequent course were uncomplicated. Feeding arteries were detected in 15.2% (7/46) cases and confirmed by surgery or autopsy. Conclusions Prenatal ultrasound has the diagnostic accuracy of IEPS. Feeding arteries noted on color Doppler are strongly indicators of IEPS. Postsurgical outcomes are favorable. Key words: Ultrasonography, prenatal; Intraabdominal extralobar pulmonary sequestration

Intraabdominal extrapulmonary sequestration in an infant diagnosed by color Doppler ultrasound

Intra-abdominal extralobar pulmonary sequestration is seen very rarely. When an echogenic mass with cystic spaces below the diaphragm in an infant is seen with ultrasound, color Doppler technique should be used to demonstrate the feeding artery. We present a case of intra-abdominal extrapulmonary sequestration in an infant that was diagnosed by color Doppler ultrasound.

Computed tomography-assisted angiography in the differential diagnosis of extralobular pulmonary sequestration in newborns

Relevance. Pulmonary sequestrations are rare pathology and make from 0.15 to 6.4 % of all congenital abnormality. Thus intra-abdominal localization of this malformation is described only in 2.5 % of all pulmonary sequestrations. Objective. Reflect the difficulty of differential diagnosis of rare lung malformation in newborns. Materials and methods. 2 cases of the extralobar sequestration located under the diaphragm diagnosed for newborns in a children's hospital for the last 20 years are in details described. Results. The diagnosis of an intra-abdominal extralobular pulmonary sequestration was finalized only after surgical treatment, confirmed histologically. Questions of differential diagnostics of rare congenital pulmonary malformations are discussed with tumors of suprarenal localization at newborns, comparison of own results to data of literature. Conclusions. In the differential diagnosis of suprarenal lesions at newborns it is necessary to consider the possibility of intra-abdominal extralobar pulmonary sequestration, especially in the localization of pathological changes at the left side.

Diagnosis of Intra-Abdominal Extralobar Pulmonary Sequestration by means of Ultrasound in a Neonate

Pulmonary sequestration is a congenital abnormality consisting of a mass of pulmonary tissue that presents an abnormal connection with the tracheobronchial tree, with a blood supply coming from an anomalous artery derived from the systemic circulation. Extralobar pulmonary sequestration is characterized by having pleural coverings that are independent of the normal lungs, with vascular supply usually coming from the aorta or from one of its branches. This diagnosis can be suspected prenatally if an abdominal mass, generally below the diaphragm, is seen. Here, we present a case of a neonate on the second day of life, with ultrasonography showing extralobar pulmonary sequestration located above the left adrenal gland that prenatally simulated a neuroblastoma.

Intra-abdominal extralobar pulmonary sequestration presenting antenatally as a suprarenal mass

Extralobar pulmonary sequestration is a rare pulmonary parenchymal anomaly which rarely may be present in an intra-abdominal location. The authors report a case of intra-abdominal extralobar pulmonary sequestration which presented to us as an antenatally diagnosed suprarenal mass and was worked up as such. The diagnosis was revealed only at laparotomy. Intra-abdominal extralobar pulmonary sequestration should also be kept in differential diagnosis in cases of masses in the suprarenal location, especially on the left side.

Intra-abdominal pulmonary sequestration: a benign suprarenal mass

A 34-year-old white woman presented with an 8.5-cm left suprarenal mass. Evaluation revealed normal adrenal hormone function. Pathologic examination after surgical removal revealed a rare benign condition, intra-abdominal extralobar pulmonary sequestration (accessory lung).

Prenatal sonographic detection of intra‐abdominal extralobar pulmonary sequestration: Report of three cases and literature review

Three cases of intra-abdominal extralobar pulmonary sequestration detected antenatally by ultrasound are reported. One case was associated with a large left diaphragmatic hernia. Sonographically, all the cases were found in the left supra-renal region presenting as a well-defined echogenic mass with cystic hypoechoic areas. The condition should be considered in the differential diagnosis of all antenatally detected upper abdominal echogenic masses, particularly when associated with a diaphragmatic hernia. Postnatal ultrasound-guided fine needle aspiration biopsy in one case yielded respiratory type epithelium and this procedure could provide a reasonably confident diagnosis of the lesion.

Imaging of prenatally detected intra-abdominal extralobar pulmonary sequestration

Intra-abdominal extralobar pulmonary sequestration is a rare congenital anomaly which may present as an abdominal mass. We describe a case of intra-abdominal extralobar pulmonary sequestration detected prenatally as a left suprarenal mass. The ultrasound, computed tomography and magnetic resonance imaging findings are illustrated and correlated with the pathologic findings.