Dravet syndrome is a progressive epileptic encephalopathy, which was described by Dravet as severe myoclonic epilepsy of infants. The main clinical features of this syndrome include: prolonged febrile seizures that begin in the first year of life, a secondary phenomenon of myoclinical or other seizure types, and regression of psychomotor functions. By the end of the first year of life, EEG during waking and sleeping is usually normal. Rhythmic, 4–5 Hz theta activity can occur at centro-parietal regions and in the vertex. Paroxysmal abnormalities are rarely registered. The slowing of background activities, dependent upon the frequency and duration of seizures, as well as pharmacological treatment, occurs between the age 2 and 5. Paroxysmal abnormalities consisting of spikes, spike wave and multiple spike waves are recorded. These changes can appear as generalized – symmetrical or asymmetrical, solitary or grouped discharges. There are also some localized sharp waves, slow waves and spikes. Intermittent photic stimulation and photic stimulation by geometric shapes provoke discharge in about 40% of patients. This finding may be positive, even during the first year of life, but not constant during the illness.