Chondroid syringoma (CS) is a rare tumor of the apocrine or eccrine glands. CS of the scalp is rare, and its clinical manifestations are similar to those of dermoid cyst, which is a common misdiagnosis for this disease. A 26-year-old woman presented with a 2-month history of an asymptomatic subcutaneous mass on the scalp. The lesions increased progressively over time. Dermatological examination showed that there was a subcutaneous mass, ranging from 2x2 cm in diameter, with a clear boundary. The surface of the skin was smooth without ulceration or scaling. Histopathologic examination was consistent with the diagnosis of CS. CS is a rare tumor of the apocrine or eccrine glands. It usually presents as a wellcircumscribed and single subcutaneous masses. Histopathology showed the tumor was located in the dermis, with nests, sheets, and cords of basal-like cells, mucin deposition, and chondroid structures. We herein report a case of CS located in the scalp. CS of the scalp is rare, and its clinical manifestations are similar to those of dermoid cyst, for which it is commonly misdiagnosed.