Bilateral Arachnoid Cysts Research Articles

Bilateral middle cranial fossa arachnoid cysts with temporal lobe agenesis. Case report in adult.

Background: The temporal lobe agenesis syndrome is a rare congenital abnormality. Bilateral temporal lobe agenesis along with middle cranial fossa arachnoid cysts is extremely rare, and only very few cases have been reported in the literature. Case report: We present the case of 21-year-old child with bilateral arachnoid cysts and temporal lobe agenesis whose mental examination and neurologic assessment is normal. The Magnetic resonance imaging (MRI) findings revealed bilateral temporal lobe agenesis with bilateral arachnoid cysts. Brain MRI sequence showing bilateral middle cranial fossa arachnoidal cysts, following CSF signal intensity on MRI. Bilateral middle cranial fossa arachnoid cysts with temporal lobe agenesis. The patient was managed conservatively. Conclusion: Bilateral middle cranial fossa arachnoid cysts with temporal lobe agenesis in adult is very rare. The diagnosis is made by brain MRI. Prophylactic surgery in asymptomatic cases is not advisable. These patients must be followed by the practician. The patient and his family must be sensualized and informed of some precautions, especially brain head trauma.

Rapid head growth in a baby with ADPKD: Answers

I. Obstructive hydrocephalus—possibly due to blood from a sub-arachnoid hemorrhage secondary to an intra-cranial aneurysm II. Tuberous sclerosis, which may be associated with ADPKD III. Space-occupying lesions such as teratomas, astrocytic tumors, or primitive neuroectodermal tumors IV. Dural arterio-venous malformation V. Arachnoid cyst VI. Benign macrocrania of infancy 2. The magnetic resonance imaging (MRI) brain scan (Fig. 1) shows collections of fluid with visible septations over the frontal lobes. There is no midline shift. The fluid displays the same density as cerebrospinal fluid and the radiological appearances are consistent with a diagnosis of bilateral frontal arachnoid cysts. 3. The management involves a conservative approach with:

Bilateral temporal lobe agenesis with bilateral arachnoid cysts – a rare congenital anomaly

Bilateral temporal lobe agenesis/hypogenesis along with middle cranial fossa arachnoid cysts (ACs) is extremely rare, and very few cases have been reported in the literature. We present the case of 2-year-old female presenting with chief complaints of headache, vomiting, and fever. There was a history of premature delivery in the seventh month and up-rolling of eyes since birth. Magnetic resonance imaging findings revealed bilateral temporal lobe agenesis with bilateral ACs, along with encephalomalacia in both parietal lobes. Ultrasound abdomen findings and biochemical tests revealed renal parenchymal disease. The lipid profile analysis revealed highly elevated triglyceride levels to 457.4 mg% and also enhanced very-low-density lipoprotein levels to 91.5 mg%. Presently, the patient is being treated on conservative lines. To our knowledge, this is the first report of an unusual association between bilateral temporal lobe agenesis associated with renal parenchymal disease and dyslipidaemia.

Bilateral Retrocerebellar Arachnoid Cysts Exerting Mass Effect and Associated With Cerebellar Tonsillar Ectopia in an Otherwise Healthy Adult

Rarely, midline or unilateral posterior fossa arachnoid cysts (ACs) exert local mass effect resulting in the symptoms and signs of cerebellar and brainstem dysfunction. These cysts are sometimes seen in conjunction with cerebellar tonsillar ectopia (TE), although the relationship between these two entities is unclear. Bilateral ACs in the posterior fossa are virtually unprecedented. We describe the case of a 33-year-old man with a history of multiple minor head injuries observed to harbour asymptomatic, bilateral cerebrospinal fluid-density collections over the cerebellar hemispheres. Six years later, he presented with headaches, limb paraesthesias, and drop attacks. Computed tomography, magnetic resonance imaging, and operative findings during burrhole drainage of the lesions showed bilateral posterior fossa ACs, with associated cerebellar TE of 11 mm. The cysts partially recurred, necessitating reopening of the burrholes, after which the patient's symptoms resolved entirely. We then discuss the challenges in diagnosing this unusual case, the relationship between AC and TE, and the role of minor head injury in the symptomatic progression of AC.

P-1339 - Agoraphobia hemiparesis and hemihypesthesia in a transsexual patient - case report

Transsexualism is a gender identity disorder soon to be removed from the DSM criteria for mental disorders. The actual developmental/congenital origin of the disorder has yet to be established. One of the theories involves morphological and neuro-hormonal modification in the corpus callosum as a possible substrate. Diagnostic assessment of a 22 year old female - male transsexual patient with a history of agoraphobia and migraine, reporting intermittent symptoms of numbness of left side of body and cheek and headaches. Data on personal/family history was obtained and neurological examination was performed. MRI scan was acquired with a 1.5 T Siemens Magnetom system with a standard head coil. Sagittal three-dimensional 3D RAGE, contiguous 1.0 mm slices, 1 acquisition sequences were obtained. Results and discussion: Family history of anxiety disorder was confirmed. Symptoms appeared following reduction of anxiolytic medication and emotional crisis. Neurological status showed signs of left pyramid deficit. NMR scan findings showed bilateral arachnoid cysts in genu corpus callosum probably of congenital origin. Co-morbidity versus concomitant disorders of psychiatric, neurological and congenital origin were discussed.

Bilateral Meckel's Cave Arachnoid Cysts With Extension to the Petrous Apex in a Patient With a Vestibular Schwannoma

Bilateral Meckel's Cave Arachnoid Cysts With Extension to the Petrous Apex in a Patient With a Vestibular Schwannoma

Bilateral Temporal Arachnoid Cysts Associated With Tuberous Sclerosis Complex

The association between tuberous sclerosis complex and intracranial abnormalities such as hemimegalencephaly, schizencephaly, intracranial arterial aneurysms, and corpus callosum agenesis/dysplasia has been reported in the recent literature. However, the association between tuberous sclerosis complex and bilateral temporal arachnoid cysts has not been reported. A case of an 8-year-old boy with a mental impairment and epileptic seizures that began 5 years earlier is presented. The neuro-radiological findings are consistent with tuberous sclerosis complex associated with bitemporal arachnoid cysts. His epileptic seizures were treated with antiepileptic medications. To the authors' knowledge, this is the first reported case of tuberous sclerosis complex associated with bilateral arachnoid cysts of the temporal region. In such cases, arachnoid cysts may exacerbate the clinical picture.

Brucellar brain abscess and bilateral arachnoid cysts, unilaterally complicated by subdural haematoma

Arachnoid cysts are benign developmental cysts that occur along the cerebrospinal axis. Brucellar abscesses in the brain are relatively uncommon, with only a few cases reported in the literature. We report here a patient with a brucellar brain abscess and bilateral arachnoid cysts (one complicated with subdural haemorrhage), who was successfully managed with craniotomy and antibiotics.

Pediatric orbital multifocal cavernous hemangiomas associated with bilateral arachnoid cysts of the middle cranial fossa

Cavernous hemangiomas of the orbit are benign vascular growths that commonly occur in adults and account for 6% of all intraorbital tumors. Multifocal intraorbital cavernous hemangiomas are quite rare. The reported incidence of arachnoid cysts accounts for only 1% of lesions that occupy intracranial space, and they are nearly always sporadic and single. So far, the authors have not encountered any study reporting the coexistence of bilateral arachnoid cysts of the middle cranial fossa and orbital multifocal cavernous hemangiomas. In this report, they describe a 10-year-old boy with such a hemangioma that included the eyelid, conjunctiva, and retrobulbar space. His was the first case of a surgically treated pediatric orbital multifocal cavernous hemangioma associated with bilateral arachnoid cysts of the middle cranial fossa. An association between arachnoid cysts, intracranial cavernous malformations, and bilateral arachnoid cysts and metabolic disorders has been reported. The authors report on the coexistence of orbital multifocal cavernous hemangiomas and bilateral arachnoid cysts of the middle cranial fossa. Based on these observations, they believe that all patients with bilateral temporal arachnoid cysts should be screened for genetic disorders. In addition, the possibility of orbital cavernous malformations should be kept in mind for the follow-up period, and patients should be evaluated for possible symptoms of this condition.

Quistes aracnoideos silvianos, hipoplasia de lóbulos temporales y encefalopatía epiléptica.

The authors describe a 14 year-old boy with bilateral arachnoid cysts of the sylvian area and temporal lobe hypoplasia. Also showed vermis and brainstem hypoplasia. Clinically manifest a severe encephalopathy with tetraparesia, autism and late onset polymorphic epilepsy. He presented a favorable outcome with valproate and vigabatrine. To the best of our knowledge only one case like ours has been reported.

Bilateral arachnoid cysts of the sylvian region in female siblings with glutaric aciduria type I

Two sisters, aged 6 and 2 1/2 years, presented with macrocephaly and delayed motor development and were found on computerized tomography to have bilateral arachnoid cysts of the sylvian region. Cystoperitoneal shunting of the larger cysts resulted in considerable neurological improvement in both children. Subsequent screening of the patients' urine for organic acids showed that the two sisters were suffering from glutaric aciduria type I (GA-I). To the best of the authors' knowledge, this is the first report to provide clear radiological and surgical evidence of the association between GA-I and bilateral arachnoid cysts of the sylvian region. The role of the shunting procedure used in these cases is discussed.

Glutaric Aciduria Type 1: First Reported Cases in Three Saudi Patients

The clinical and biochemical findings in three patients with glutaric aciduria Type 1 (GAT1) are presented. They had a normal postnatal period of three to 14 months. They developed sudden and severe encephalopathy following an infection or trauma (patient 3) that gradually progressed to severe dystonia, choreoathetosis, spastic quadriplegia and mental retardation. Neuroradiologic studies of the brain revealed white matter disease and frontotemporal lobe hypoplasia. The urine findings by gas chromatography/mass spectrometry (GC)/(MS) were characteristic of GAT1. Since GAT1 is an organic acidemia without intermittent acidotic attacks, but primarily manifests with progressive encephalopathy, it is important to recognize the potential of its existence among handicapped children in chronic care facilities. The good clinical response in two of the patients urges early diagnosis in subsequent newborn siblings of the families with the disease. The diagnosis of three patients in less than two years indicates the need for neonatal screening for the recognition of this disease, among other treatable metabolic diseases, in Saudi Arabia.

Unusual Intra- and Extracranial Arteriovenous Communication

The authors report an unusual case of arteriovenous communication between extracranial and intracranial vessels, accompanied by incidentally detected bilateral arachnoid cysts of the middle cranial fossa. A 52-year-old male was admitted with a sudden onset of headache, vomiting, and conjunctival hyperemia of the right eye followed by progressive chemosis and proptosis. He had undergone a craniotomy for hypertensive right putaminal hemorrhage 4 months previously. Angiography showed the main feeding artery to be the superficial temporal artery and the draining veins to be the superficial Sylvian veins and the basal vein of Rosenthal. Partial obstruction of the right cavernous sinus was also shown. At surgery, granulation tissue continued to the dura mater through the skull aperture of previous craniotomy and adhered to the underlying damaged cerebrum. The extremely unusual nature of the communication, the operative findings, and the atypical fistulous figures suggested that communication had occurred postoperatively via newly generated vessels in granulation tissue.

Kl??ver-Bucy syndrome in a child with bilateral arachnoid cysts

Kl??ver-Bucy syndrome in a child with bilateral arachnoid cysts

Arachnoid cyst of the middle cranial fossa: Report of bilateral cysts in siblings

Primary intracranial arachnoid cysts are not too infrequent, but cases involving a familial occurrence of arachnoid cysts or bilateral symmetrical cysts in one patient have rarely been reported. We report bilateral arachnoid cysts of the middle cranial fossa in siblings.