Atrophoderma vermiculata is a rare and benign follicular disorder of the skin occurs due to abnormal keratinisation in follicular pilosebaceous unit. It presents as multiple, symmetric, depressed pitted scars with reticular/ honeycomb atrophy of skin. It usually presents in face but in our case lesions are seen over chest, back, shoulder and gluteal region. The onset is mostly sporadic or sometimes inherited Autosomal Dominant. It is a clinical variant of Keratosis Pilaris Atrophicans. This condition is difcult to treat cosmetically. Hereby we report a rare case of Atrophoderma Vermiculatum with isolated presentation and different site involvement, treated with oral Isotretinoin showing good response