Pseudocoarctation Of Aorta Research Articles

CT Angiography for Aortic Arch Anomalies: Prevalence, Diagnostic Efficacy, and Illustrative Findings.

Aortic arch anomalies encompass a diverse spectrum of conditions. Elucidating the prevalence of these anomalies, their impact on patient wellbeing, and the most effective diagnostic tools are crucial steps in ensuring optimal patient care. This paper aims to explore the various presentations of aortic arch anomalies, emphasizing the remarkable utility of computed tomography (CT) angiography in their definitive diagnosis and characterization. We conducted a retrospective study on patients who were submitted to the CT angiography of the thoracic aorta or supra-aortic trunks, or the contrast-enhanced CT scans of the thorax and/or cervical region between January 2021 and February 2024 in our Hospital. Out of the total of 2350 patients, 18 were diagnosed with aortic arch anomalies, with an average age of approximately 55 years. The aortic arch anomalies identified in the study were as follows: left aortic arch with the aberrant origin of the right subclavian artery, right aortic arch (types I and II), double aortic arch, aortic coarctation, aortic pseudocoarctation, and ductus diverticulum. Although often asymptomatic, aortic arch anomalies require recognition and CT using advanced post-processing techniques is the optimal diagnostic method with the ability to also identify other associated cardiac or vascular malformations.

Thoracic endovascular repair for blunt traumatic thoracic aortic injury: Long-term results.

This study aims to evaluate the endoprosthesis complications in patients undergoing TEVAR for blunt traumatic thoracic aortic injury, through long-term clinical and diagnostic follow-up. During the study interval (November 2000-October 2020), a total of 38 patients (63% male; average age 37.5years) with thoracic aortic injury underwent thoracic endovascular aortic repair. Patients underwent routine follow-up with clinical examination and radiological evaluation (CT-angiography or MRI-angiography plus chest radiograph), scheduled at 1month, at 6months (only in the cases of thoracic aortic dissection), at 1year after the procedure and every 1year thereafter. Technical success was achieved in 38 procedures (100%). The TEVAR-related mortality rate was 0%. No immediate major complications related to the endovascular procedure were observed. The median duration of diagnostic follow-up was 80months. A total of four procedure-related complications (10.5%) were identified at the follow-up. Three (7.9%) distal infoldings and collapses of the thoracic endoprosthesis and one (2.6%) type Ia endoleak were observed. No thrombosis of the prosthesis, nor signs of aortic pseudocoarctation were identified. No further complications related to endograft (endoleaks, infections, rupture, partial or complete thrombosis) occurred. No changes in the native aorta, stenosis, or increases in the endograft's diameters were observed. A total of 20 patients (52.6%) underwent MRI-angiography examinations, while a total of 34 patients (89.5%) underwent chest radiographs at the follow-up. In all cases, CT-angiography examinations were performed at the follow-up. Procedure-related complications were observed within one year of TEVAR, limiting concerns related to the durability of the prosthesis. No morphological changes in the aorta were observed despite long-term follow-up. The consequences of lifelong surveillance in terms of radiation exposure deserve special consideration, especially in younger patients treated for TAI.

Unexpected Discovery of an Aortic Pseudocoarctation During Treatment for Aortic Haematoma

Unexpected Discovery of an Aortic Pseudocoarctation During Treatment for Aortic Haematoma

Aortic pseudocoarctation: a very rare finding

A 52-year-old Caucasian woman with a history of hypertension since age 30 was referred to cardiology department due to aortic stenosis. She had exertional dyspnoea, without thoracic pain or syncope....

Pseudocoarctation of Aorta with Aneurysmal Dilatation with Acute Coronary Syndrome

Pseudocoarctation of Aorta with Aneurysmal Dilatation with Acute Coronary Syndrome

Congenital kinking of aorta

Pseudocoarctation is an unusual anomaly mirroring true coarctation. Congenital kinking or pseudocoarctation of aorta was never a benign condition. Although surgical repair should be suggested for all symptomatic individuals. Regular...

Treatment of patients with posttraumatic aortic pseudocoarctation syndrome

Treatment of patients with posttraumatic aortic pseudocoarctation syndrome

Treatment of the patient with posttraumatic aortic pseudocoarctation syndrome

Treatment of the patient with posttraumatic aortic pseudocoarctation syndrome

Surgical Repair of a Pseudocoarctation with Cervical Aortic Arch Complicated by Multiple Aneurysms of the Aorta: A Case Report

Aortic pseudocoarctation is a rare congenital anomaly characterized by elongation and deformity of the aortic arch and is known to be associated with aneurysmal formation. Several studies unite to say it leads to a surgical sanction as soon as symptomatic or associated with aneurysms of the aortic arch. Our patient is a 12 years old boy, followed since birth for a little tight pseudocoarctation with a cervical aortic arch and transverse aortic arch hypoplasia. Close clinical and Para clinical monitoring including angioscans, showed the gradual enlargement of the superior mediastinum, in relation with the appearance of three aneurysms of the aortic arch. The intervention, performed by sternotomy, has consisted of the resection of the aneurysmal area and the interposition of a Dacron tube to repair the aortic arch and the implantation of the left subclavian artery into the left carotid artery. The postoperative course was uneventful. Management of pseudocoarctation associated with cervical aortic arch and aneurysms remains surgical. Close monitoring of patients with pseudocorctation, seems to be essential to avoid fatal complications such as aneurysmal rupture.

PP04.13 – 2780: The association of Moya Moya disease with pseudocoarctation: A case report

Objective Moya Moya disease is characterized by the progressive occlusion of the cerebral arteries at the circle of Willis, leading to formation of abnormal networks of small collateral vessels with a “puff of smoke” appearance on angiography. The classic pattern involves the distal internal carotid arteries bilaterally, but unilateral variants and involvement of additional anterior and posterior circulation vessels are well described. Coarctation of aorta is a rare association in Moya Moya disease. We present a case of Moya Moya disease and pseudocoarctation of aortic arch. Methods A 7-year-old girl was admitted with a brief loss of consciousness. History revealed clumsyness and frequent falls. All her developmental milestones were delayed comparing peers. Physical examination revealed slight left sided hemiparesis, dysmetria and dysdiadokinesia on the left side. Her EEG was normal. Brain magnetic resonance imaging (MRI) showed encephalomalacia in the right occipital lobe and conventional cerebral angiography revealed occlusion in several arteries including bilateral internal carotid arteries, bilateral anterior cerebral arteries, and bilateral posterior cerebral arteries and diffuse collateral vessels with a puff of smoke appearance. In echocardiographic study, aortic arch and isthmus was tortous, a gradient of 45 mmHg was measured between the proximal and distal parts of coarctation site by CW Doppler. Coarctation of aorta was suggested. Catheter angiography showed large dilated aortic arch kinking at before origin of left subclavian artery, without any pressure difference between the proximal and distal parts, pseudocoarctation was diagnosed. Aspirin was started for prevention of subsequent cerebral embolism. Results The diagnosis of Moya Moya disease was made based on conventional cerebral angiography findings. Conclusion The association of Moya Moya disease with aortic pseudocoarctation may be related to an extensive systemic involvement of blood vessels. Careful evaluation of children with Moya Moya disease is necessary to detect aortic coarctation.

大動脈弁狭窄症および偽性大動脈縮窄症に合併した胸部大動脈瘤に対して clamshell 切開により同時手術を施行した1例

大動脈弁狭窄症および偽性大動脈縮窄症に合併した胸部大動脈瘤に対して clamshell 切開により同時手術を施行した1例

Thoracic Aortic Aneurysm With Aortic Pseudocoarctation Involving the Left Subclavian Artery

A 39-year-old man with a thoracic aortic aneurysm and pseudocoarctation underwent graft replacement of the distal arch. The left subclavian artery, which rose just after the aneurysm, was also reconstructed at surgery. The aneurysmal wall was extremely thin, and the adventitia and a small amount of medial tissue were found on histologic examination. Thus, surgical treatment was recommended due to risk of rupture. Furthermore, because aneurysms involved the cervical branch, separate reconstruction was also performed. Endovascular intervention is not appropriate for this group of patients because of the complex kinking of the aorta and the extremely thin aneurysmal wall.

Pseudocoarction of the aorta and crossed fused ectopic kidney assessed by multidetector computed tomography

Aortic pseudocoarctation is a congenital abnormality consisting of an elongated aortic arch with a kink at level of the isthmus. However, unlike coarctation, significant flow obstruction is not associated with pseudocoarctation, although there is an increased incidence other cardiovascular anomalies. This case demonstrates the use of multidetector CT as part of the clinical evaluation of a 49-year-old male with suspected aortic coarctation, leading to the final diagnosis of pseudocoarctation, as well as the incidental discovery of a crossed fused ectopic kidney.

An incidental finding while investigating secondary hypertension: severe abdominal aortic pseudocoarctation.

A 46-year-old female patient presented with uncontrolled hypertension to investigate a possible secondary underlying cause. Her hypertension was incidentally diagnosed when she was being evaluated preoperatively for uterine fibroma. She had no family history of hypertension. Her initial blood pressure was 190/110 mmHg from both arms. No abdominal bruit was audible over the trajectory of renal arteries or abdominal aorta. Bilateral upper and lower extremity arterial pulses were symmetrically palpated. We performed renal Doppler ultrasound along with endocrinologic work-up. Doppler ultrasound of the kidney revealed normal renal arteries and a kinking in the infrarenal part of the abdominal aorta. Thus, we performed magnetic resonance angiography of the abdominal aorta and renal arteries to further clarify the aforementioned findings on ultrasound. It revealed leftward severe abdominal aortic kinking below the renal arteries’ origins (Figure ​(Figure1).1). No mass lesion was seen to depress the aorta. All other work-ups proved to be unremarkable in terms of revealing an underlying cause for the patient's hypertension. We managed to control the hypertension with olmesartan 40 mg qid, bisoprolol 10 mg qid and amlodipin 10 mg qid treatment. Fig. 1 Magnetic resonance imaging of abdominal aorta shows severe leftward kinking of abdominal aorta below the renal artery origins. Abdominal aortic pseudocoarctation is a very rare developmental abnormality. To the best of our knowledge, only a few cases have been published in the literature to date [1,2]. The throasic form of the condition that is much more prevalent usually involves the aortic arch and may be associated with pseudoaneurism formations [3,4]. This abnormality is benign and does not cause a luminal narrowing or abnormal collaterals and most of the time remains asymptomatic. Conflict of interest statement. None declared.

Late thrombosis of a thoracic aorta stent graft: Therapeutic management

The case of a 17-year-old adolescent boy with severe polytrauma is reported. Among other injuries, he presented with aortic rupture distal to the origin of the subclavian artery with no bleeding into the mediastinum. The lesion was repaired by placement of a Cook TX2 endovascular graft (Cook Incorporated, Bloomington, Ind). One year later, he was hospitalized with acute heart failure. Computed tomography angiography showed nearly complete stent graft occlusion and no evidence of altered integrity of the device. A right axillofemoral bypass was performed, allowing conversion to successful definitive repair consisting of an extra-anatomic bypass from the ascending aorta to the supraceliac abdominal aorta.

Aortic Pseudocoarctation Associated With a Stenotic Congenitally Bicuspid Aortic Valve

The diagnosis of aortic coarctation is when a high-velocity Doppler jet is seen in the proximal descending aorta. Such a jet was seen in a 23-year-old man with bicuspid aortic valve complicated by severe aortic insufficiency in the presence of a normal aorta with slight tapering confirmed by magnetic resonance imaging. After aortic replacement, the gradient was no longer seen. In conclusion, high flow in the aorta induced by large regurgitant volumes can result in the appearance of "relative stenosis" or pseudocoarctation.

Right Cervical Aortic Arch and Pseudocoarctation of the Aorta Associated with Aneurysms and Steal Phenomena: US, CTA, and MRA Findings

A 55-year-old woman presented with right cervical aortic arch with pseudocoarctation of the aorta further complicated by the presence of multiple aneurysms and a high-grade stenosis at the origin of the left subclavian trunk from the aorta causing a discrepancy in blood pressure between the right and left arms. The branching pattern and the resulting complex steal syndromes involving the left carotid and the subclavian system are unique. The computed tomography angiography, magnetic resonance angiography, and Doppler ultrasound findings are described.

Aortic pseudo-coarctation: spiral volumetric computed tomography imaging

Aortic pseudo-coarctation is a quite rare cardiovascular malformation characterized by a redundant and severely kinked aortic arch without a significant transisthmic pressure gradient. Diagnostic assessment is usually performed by angiography or other imaging techniques.